King Abdullah University Hospital Faculty of Medicine, Jordan University of Science and Technology (JUST), P. O. Box 22110, Irbid, 3030, Jordan,
Hernia. 2014 Jun;18(3):427-9. doi: 10.1007/s10029-014-1222-z. Epub 2014 Feb 5.
Congenital massive hiatus hernia (CMHH) is an uncommon disorder during childhood. It can be associated with grave complications especially if presented in the highest grade; type IV, when the hernia contains other intra-peritoneal organ beside the stomach through a large hiatus defect. The insidious form of clinical presentation can be deceptive in diagnosis and may mimic congenital diaphragmatic hernia or other chest pathologies. The basic principle of surgical repair is to reduce the herniated organs, excise the hernia sac, and repair the crural defect and to add anti-reflux procedure with or without gastropexy. Traditionally, this has been done by open approach. Nowadays, the minimally invasive approach is the preferred method of treatment. A sixteen-month-old boy with history of recurrent respiratory symptoms was diagnosed with CMHH type IV for which laparoscopic repair was performed. Few reports in using minimally invasive technique in the management of CMHH in the pediatric age group are present in the literature, to the best of our knowledge type IV had never been described in young infants. We present a new case repaired by laparoscope in a young infant with CMHH type IV from the Middle East.
先天性巨大裂孔疝(CMHH)是儿童期一种罕见的疾病。它可能与严重的并发症有关,特别是当它表现为最高等级(IV 型)时,即疝通过大裂孔缺陷包含胃以外的其他腹腔内器官。隐匿的临床表现形式可能在诊断上具有欺骗性,并可能模拟先天性膈疝或其他胸部病变。手术修复的基本原则是减少疝出的器官,切除疝囊,修复裂孔缺陷,并添加抗反流手术,无论是否进行胃固定术。传统上,这是通过开放方式完成的。如今,微创方法是首选的治疗方法。一名 16 个月大的男孩因反复呼吸道症状就诊,被诊断为 IV 型 CMHH,为此进行了腹腔镜修复。据我们所知,目前文献中仅有少数关于微创技术在小儿 CMHH 管理中的应用报道,从未在婴幼儿中描述过 IV 型。我们报告了一个新的病例,一名来自中东的 16 个月大的婴儿,患有 IV 型 CMHH,通过腹腔镜进行了修复。