Bhagat Sanjeev, Varshney Saurabh, Bist Sampan S, Gupta Nitin
Sanjeev Bhagat, Department of ENT, Government Medical College, 7-D Rajindra Hospital, Patiala (Punjab) 147001, India.
Ear Nose Throat J. 2014 Mar;93(3):E1-3.
Schwannomas are rare, benign, slowly growing neurogenic tumors that originate in peripheral, spinal, or cranial nerves other than the optic and olfactory nerves. In the head and neck, these tumors usually arise from the vagus nerve and the cervical sympathetic chain in the parapharyngeal space. Cervical sympathetic chain schwannomas represent a rare subgroup of schwannomas; fewer than 60 cases have been reported in the literature. These tumors are rarely seen in children and adolescents. Because patients typically present with an asymptomatic neck mass and vague complaints, clinical suspicion is important in making the diagnosis. Neural deficits at presentation are uncommon. The presence of features of Horner syndrome before excision is very rare, having been previously reported in only 10 cases of cervical sympathetic chain schwannoma. We report an extremely rare case of a cervical sympathetic chain schwannoma in a child who presented with Horner syndrome. The lesion was successfully excised.
施万细胞瘤是一种罕见的良性、生长缓慢的神经源性肿瘤,起源于除视神经和嗅神经外的周围神经、脊神经或颅神经。在头颈部,这些肿瘤通常起源于迷走神经和咽旁间隙的颈交感神经链。颈交感神经链施万细胞瘤是施万细胞瘤中一个罕见的亚组;文献报道的病例不到60例。这些肿瘤在儿童和青少年中很少见。由于患者通常表现为无症状的颈部肿块和模糊的主诉,临床怀疑对于做出诊断很重要。就诊时出现神经功能缺损并不常见。切除前出现霍纳综合征特征的情况非常罕见,此前仅有10例颈交感神经链施万细胞瘤的相关报道。我们报告了一例极为罕见的儿童颈交感神经链施万细胞瘤病例,该患儿表现为霍纳综合征。病变已成功切除。