Arslan Ahmet Hulusi, Ugurlucan Murat, Yildiz Yahya, Ay Sibel, Bahceci Fatma, Besikci Resmiye, Cicek Sertac
Anadolu Medical Center Hospital, Center for Heart and Vascular Care, Section of Cardiovascular Surgery, Gebze, Kocaeli, Turkey.
World J Pediatr Congenit Heart Surg. 2014 Apr;5(2):211-5. doi: 10.1177/2150135113516370.
Common arterial trunk (persistent truncus arteriosus) is a rare cardiac defect requiring surgical repair early in life because of the fast development of pulmonary vascular obstructive disease. We present our institutional experience with patients having common arterial trunk who are diagnosed after one year of age.
Between August 2010 and May 2013, a total of 1,436 patients were treated for congenital cardiac defects at our institution. Common arterial trunk was treated surgically in seven patients older than one year of age (three males, four females; age: 13 months to 5 years, mean: 2.8 ± 2.04 years). All patients underwent cardiac catheterization in order to determine operability.
All patients had the aortic dominant type of common arterial trunk. The pulmonary vascular resistance and Qp/Qs ratio before and after oxygen inhalation were mean 9.04 + 4.2 (range: 3.8 and 10.7) wood units and 4.67 ± 2.3 (range: 3 and 6.5) wood units and 3.3 + 1.8 (range: 1.42 and 5.3) and 4.98 + 2.2 (range: 4 and 6.2), respectively. All patients underwent elective primary repair. The ventricular septal defect was closed in all patients, five with a nonvalved patch and two with a unidirectional check-valved patch. Early postoperatively, patients were sedated, hyperventilated, and received nitric oxide for a minimum of 24 hours. There was no early or late mortality. The mean length of hospital stay was 9.3 ± 5.7 days, and mean duration of follow-up was 214 ± 59 days.
Complete repair of common arterial trunk in patients older than one year of age is feasible in appropriately selected cases. Preoperative cardiac catheterization to assess reactivity of the pulmonary vascular bed is important as are appropriate strategies for postoperative management. Together, these elements make it possible to achieve primary repair with excellent outcomes despite late presentation.
共同动脉干(永存动脉干)是一种罕见的心脏缺陷,由于肺血管阻塞性疾病发展迅速,需要在生命早期进行手术修复。我们介绍了本机构对1岁以后诊断为共同动脉干的患者的治疗经验。
2010年8月至2013年5月,共有1436例先天性心脏缺陷患者在本机构接受治疗。7例1岁以上的患者(3例男性,4例女性;年龄:13个月至5岁,平均:2.8±2.04岁)接受了共同动脉干的手术治疗。所有患者均接受心脏导管检查以确定手术可行性。
所有患者均为主动脉优势型共同动脉干。吸氧前后的肺血管阻力和Qp/Qs比值分别为平均9.04 + 4.2(范围:3.8至10.7)伍德单位和4.67±2.3(范围:3至6.5)伍德单位以及3.3 + 1.8(范围:1.42至5.3)和4.98 + 2.2(范围:4至6.2)。所有患者均接受了择期一期修复。所有患者的室间隔缺损均已闭合,5例使用无瓣补片,2例使用单向止回瓣补片。术后早期,患者接受镇静、过度通气,并至少接受24小时一氧化氮治疗。无早期或晚期死亡病例。平均住院时间为9.3±5.7天,平均随访时间为214±59天。
在适当选择的病例中,对1岁以上患者进行共同动脉干的完全修复是可行的。术前进行心脏导管检查以评估肺血管床的反应性很重要,术后管理的适当策略也同样重要。尽管就诊较晚,但这些因素共同作用使得实现一期修复并取得良好效果成为可能。