Chiostri Benjamin, Piccinini Fernando, Vrancic Mariano, Klinger Daniel, Navia Daniel, Lalor Nicolas, Longo Francisco, Kreutzer Christián
Services of Pediatric Cardiac Surgery, Sanatorio Anchorena, Buenos Aires, Argentina
Adult Cardiac Surgery, Sanatorio Anchorena, Buenos Aires, Argentina.
World J Pediatr Congenit Heart Surg. 2014 Jul;5(3):467-9. doi: 10.1177/2150135114526419.
We report a challenging case of a 32-year-old patient in New York Heart Association (NYHA) class IV with pulmonary atresia, ventricular septal defect, a left aortopulmonary collateral artery, a right modified Blalock-Taussing shunt, and a gigantic aneurysm of the ascending aorta with severe aortic valve insufficiency. A combined Rastelli and Bentall procedure was performed by a joint adult and pediatric cardiovascular surgery team. One year after the operation, the patient is in NYHA class I, working full time.
我们报告了一例具有挑战性的病例,患者为一名32岁男性,纽约心脏协会(NYHA)心功能IV级,患有肺动脉闭锁、室间隔缺损、左主动脉肺动脉侧支动脉、右改良布莱洛克 - 陶西格分流术,以及升主动脉巨大动脉瘤合并严重主动脉瓣关闭不全。一个成人与儿科心血管外科联合团队实施了Rastelli手术与Bentall手术相结合的手术。术后一年,患者NYHA心功能I级,已全职工作。