Chandra Sadanandavalli Retnaswami, Issac Thomas Gregor
Department of Neurology, National Institute of Mental Health and Neurosciences, Bangalore, Karnataka, India.
Department of Clinical Neurosciences, National Institute of Mental Health and Neurosciences, Bangalore, Karnataka, India.
J Neurosci Rural Pract. 2014 Apr;5(2):189-90. doi: 10.4103/0976-3147.131679.
Pseudodystonia is the term used to define abnormal postures, which are not due to the disorders of the basal ganglia and is encountered very rarely in clinical practice and often difficult to distinguish from true dystonia syndromes. We report a rare case of a battered woman who was managed as restricted resistant dystonia with pharmacotherapy and intrathecal baclofen and referred for considering deep brain stimulation (DBS). The patient turned out to be a case of pseudodystonia due to bilateral hip dislocation. This was due to assault by a close relative and the history was masked by the patient for more than one and a half years. In a patient with late onset dystonia, who is resistant to the recommended treatment for dystonia along with atypical clinical features and electrophysiological parameters, pseudodystonia should always be considered as a possible diagnosis and evaluated for causes of the same.
假性肌张力障碍是用于定义异常姿势的术语,这些姿势并非由基底神经节疾病引起,在临床实践中很少见,且常常难以与真性肌张力障碍综合征相区分。我们报告了一例罕见的受虐妇女病例,该患者最初被当作对药物治疗和鞘内注射巴氯芬耐药的局限性肌张力障碍进行处理,并被转诊考虑接受脑深部电刺激(DBS)治疗。结果发现该患者是由于双侧髋关节脱位导致的假性肌张力障碍。这是由一名近亲的袭击所致,而患者隐瞒病史长达一年半以上。对于起病较晚、对推荐的肌张力障碍治疗有抵抗且伴有非典型临床特征和电生理参数的肌张力障碍患者,应始终将假性肌张力障碍视为一种可能的诊断,并对其病因进行评估。