腹部丛状神经纤维瘤在计算机断层扫描上模拟腹膜假黏液瘤。

Abdominal plexiform neurofibromatosis simulating pseudomyxoma peritonei on computed tomography.

作者信息

Mirich D R, Gray R R, Grosman H

机构信息

Department of Diagnostic Radiology, Wellesley Hospital, University of Toronto, Ontario, Canada.

出版信息

J Comput Assist Tomogr. 1989 Jul-Aug;13(4):709-11. doi: 10.1097/00004728-198907000-00034.

DOI:10.1097/00004728-198907000-00034

PMID:2501362

Abstract

We present and discuss an unusual case of extensive abdominal plexiform neurofibromatosis that simulated pseudomyxoma peritonei on CT. Multiple low density subdiaphragmatic masses caused scalloped liver margins and thickening of the mantle, which displaced bowel loops centrally, suggesting the diagnosis of pseudomyxoma peritonei. However, open biopsy revealed plexiform neurofibromatosis.

摘要

我们呈现并讨论一例罕见的广泛腹部丛状神经纤维瘤病病例，该病例在CT上模拟了腹膜假黏液瘤。多个膈下低密度肿块导致肝脏边缘呈扇贝样改变以及包膜增厚，这些肿块使肠袢向中央移位，提示腹膜假黏液瘤的诊断。然而，开放活检显示为丛状神经纤维瘤病。