Pérez-Martínez Ignacio Jaime, Mantilla-Morales Alejandra, Cruz-Esquivel Iván, Gallegos-Hernández José Francisco
Departamento de Tumores de Cabeza y Cuello, Hospital de Oncología, CMN Siglo XXI. Instituto Mexicano del Seguro Social, Mexico DF, Mexico.
Departamento de Patología, Hospital de Oncología, CMN Siglo XXI. Instituto Mexicano del Seguro Social, Mexico DF, Mexico.
Cir Cir. 2013 Sep-Oct;81(5):436-40.
The trichilemmal carcinoma is a rare malignant neoplasm, whose origin lies in the annexes of the skin, because of its low prevalence often confused with other dermal tumors, the differential diagnosis is not easy and is usually made by exclusion; in theory, its behavior is slow with little tendency to send both regional lymph node metastasis and systemic. Due to the limited number of cases there is no consensus on the prognosis, although it is generally considered good. The aim of this report is to show a case that, contrary to previous reports, the clinical presentation is aggressive with large soft tissue tumor infiltration around the site of origin in a patient without risk factors for skin cancer.
Male patient, 65 years old with cytologic diagnosis of carcinoma in a preprarotideal facial tumor, characteristics at diagnosis were infiltration of the facial skin, ear, and parotid gland. Complete block resection was performed, radical parotiroidectomy and radical neck dissection; the soft tissue defect was covered with a pediculated flap. The evolution was satisfactory it follow-up short though. We evaluated the experience in the literature regarding the prognosis and treatment of these patients.
Trichilemmal carcinoma can be fully invasive behavior prognosis is difficult to know and probably depends on the clinical stage at diagnosis.
毛母质癌是一种罕见的恶性肿瘤,起源于皮肤附属器,因其发病率低,常与其他皮肤肿瘤混淆,鉴别诊断不易,通常通过排除法进行;理论上,其生长缓慢,很少发生区域淋巴结转移和全身转移。由于病例数量有限,对于其预后尚无共识,尽管一般认为预后良好。本报告的目的是展示一个病例,该病例与以往报告相反,临床表现具有侵袭性,在一名无皮肤癌危险因素的患者中,原发部位周围有巨大软组织肿瘤浸润。
一名65岁男性患者,腮腺前面部肿瘤的细胞学诊断为癌,诊断时的特征为面部皮肤、耳部和腮腺浸润。进行了完整的肿块切除、根治性腮腺切除术和根治性颈清扫术;软组织缺损用带蒂皮瓣覆盖。尽管随访时间短,但病情进展令人满意。我们评估了文献中关于这些患者预后和治疗的经验。
毛母质癌可能具有完全侵袭性,预后难以确定,可能取决于诊断时的临床分期。