Hervás Ontiveros A, España Gregori E, Climent Vallano L, Rivas Rodero S, Alamar Velázquez A, Simal Julián J A
Unidad docente de Oftalmología, Departamento de Cirugía, Universidad de Valencia, Hospital Universitario La Fe, Valencia, España.
Unidad docente de Oftalmología, Departamento de Cirugía, Universidad de Valencia, Hospital Universitario La Fe, Valencia, España.
Arch Soc Esp Oftalmol. 2015 Jan;90(1):22-5. doi: 10.1016/j.oftal.2014.02.010. Epub 2014 Nov 20.
The case is presented of a 21 year-old male with a history of left proptosis and diplopia of two weeks of onset. The MRI showed an ethmoid-orbital vascular lesion with anterior skull base invasion and orbital extension. Biopsy of the ethmoid confirmed fibrovascular tissue, which supported the diagnosis of angiofibroma.
It is a benign neoplasm with local characteristics of malignancy due to its ability to invade adjacent areas. In this case, the debut presented with manifestations of orbital extension. A broad and multidisciplinary approach is needed in order to improve prognosis.
该病例为一名21岁男性,有两周的左侧眼球突出和复视病史。磁共振成像显示筛窦-眶部血管性病变,侵犯前颅底并向眶内扩展。筛窦活检证实为纤维血管组织,支持血管纤维瘤的诊断。
这是一种良性肿瘤,但因其具有侵犯相邻区域的能力而具有局部恶性特征。在本病例中,首发表现为眶内扩展。为改善预后,需要采取广泛的多学科方法。