一名患有先天性膈疝的新生儿的肺毛细血管血管瘤病。

Pulmonary capillary hemangiomatosis in a neonate with congenital diaphragmatic hernia.

作者信息

Akinkuotu Adesola C, Sheikh Fariha, Cass Darrell L, Lee Timothy C, Welty Stephen E, Kearney Debra L, Olutoye Oluyinka O

机构信息

Texas Children's Fetal Center, Baylor College of Medicine, 6701 Fannin St, Suite 1210, Houston, TX, 77030, USA.

出版信息

Pediatr Surg Int. 2015 May;31(5):501-4. doi: 10.1007/s00383-015-3678-z. Epub 2015 Feb 13.

DOI:10.1007/s00383-015-3678-z

PMID:25678439

Abstract

Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary hypertension (PHTN). We present a neonate with congenital diaphragmatic hernia (CDH) and concurrent PCH. Severe PHTN was unrelenting and death occurred at 4 months. Diagnosis of PCH is challenging in the setting of CDH and portends a poor prognosis.

摘要

肺毛细血管血管瘤病（PCH）是肺动脉高压（PHTN）的一种罕见病因。我们报告一例患有先天性膈疝（CDH）并并发PCH的新生儿。严重的PHTN持续存在，患儿在4个月时死亡。在CDH背景下，PCH的诊断具有挑战性，且预后不良。