Mascarella Marco A, Schwartz Joseph, Manoukian John J
Department of Otolaryngology - Head and Neck Surgery, McGill University, Montreal, Quebec, Canada.
Department of Otolaryngology - Head and Neck Surgery, McGill University, Montreal, Quebec, Canada.
Int J Pediatr Otorhinolaryngol. 2015 May;79(5):769-72. doi: 10.1016/j.ijporl.2015.03.009. Epub 2015 Mar 18.
An array of genetic syndromes has been associated with intra-oral adhesions in neonates. The primary medical issues arise from airway obstruction, feeding difficulties and poor oral development, specifically with cleft palate lateral synechia syndrome (CPLSS). Despite this, a paucity of data exists for the clinical management of intra-oral adhesions in this population. We report the cases of a father and daughter diagnosed with CPLSS who presented with respiratory and feeding difficulties at birth undergoing surgical correction. Early surgical ligation of intra-oral bands allows for a stabilization of the airway, improved feeding and oral development with a good long-term outcome.
一系列遗传综合征与新生儿口腔内粘连有关。主要的医学问题源于气道阻塞、喂养困难和口腔发育不良,尤其是腭裂侧粘连综合征(CPLSS)。尽管如此,关于该人群口腔内粘连临床管理的数据却很少。我们报告了一对父女被诊断为CPLSS的病例,他们出生时出现呼吸和喂养困难,并接受了手术矫正。早期手术结扎口腔内系带可稳定气道、改善喂养和口腔发育,并取得良好的长期效果。