一例合并叶内型支气管肺隔离症和完全性内脏转位的病例。
A case of concomitant intralobar bronchopulmonary sequestration and situs inversus totalis.
作者信息
Barış Mustafa Mahmut, Gezer Naciye Sinem, Çelik Ahmet Orhan, Kılınç Oğuz, Balcı Pınar
机构信息
Department of Radiology, Faculty of Medicine, Dokuz Eylul University Hospital, Izmir, Turkey.
Department of Radiology, Faculty of Medicine, Süleyman Demirel University, Isparta, Turkey.
出版信息
Clin Respir J. 2017 May;11(3):391-393. doi: 10.1111/crj.12345. Epub 2015 Aug 3.
BACKGROUND AND AIMS
Situs inversus is a rare congenital abnormality involving partial or complete transposition of the thoracic or abdominal viscera. In situs inversus totalis, both the thoracic and abdominal viscera are transposed. The incidence of this condition is 0.01% to 0.02%. Bronchopulmonary sequestration (BPS) is a rare congenital abnormality of the respiratory tract with an incidence of 0.15% to 1.80%. Intralobar sequestration is uncommonly associated with congenital anomalies.
METHODS
A routine chest X-ray of a 41-year-old asymptomatic man showed dextrocardia, a left-sided liver, right-sided stomach, and left paracardiac opacity.
RESULTS
Computed tomography (CT) and CT pulmonary angiography revealed dextrocardia with situs inversus totalis and left paracardiac intralobar BPS in the lingular segment of the left upper lobe.
CONCLUSION
We present a rare case of combined situs inversus totalis and intralobar BPS with an atypical location and feeder artery.
背景与目的
内脏反位是一种罕见的先天性异常，涉及胸腹部脏器的部分或完全转位。在全内脏反位中，胸腹部脏器均发生转位。这种情况的发生率为0.01%至0.02%。支气管肺隔离症（BPS）是一种罕见的先天性呼吸道异常，发生率为0.15%至1.80%。叶内型隔离症很少与先天性异常相关。
方法
一名41岁无症状男性的常规胸部X线检查显示右位心、左侧肝脏、右侧胃和心旁左侧不透明影。
结果
计算机断层扫描（CT）和CT肺动脉造影显示全内脏反位伴右位心以及左上叶舌段心旁叶内型BPS。
结论
我们报告了一例罕见的全内脏反位合并叶内型BPS病例，其位置和供血动脉不典型。
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