Connelly Tara, Kolcow Walenty, Smyth Yvonne, Veerasingham David
Department of Surgery, Galway University Hospital, Galway, Co Galway, Ireland.
Department of Cardiothoracic Surgery, Galway University Hospital, Galway, Ireland.
BMJ Case Rep. 2015 Jul 15;2015:bcr2015211166. doi: 10.1136/bcr-2015-211166.
Unicuspid aortic valve (UAV) is a rare congenital anomaly typically affecting patients in their fourth and fifth decades and presenting with signs of heart failure. Our case is one of a previously asymptomatic teenage girl with a UAV, who presented with cardiac arrest and was successfully treated. Only two other similar cases have been reported in the literature, both were of slightly older male patients. Our case highlights the morbidity associated with the anomaly supporting the need for careful assessment of the valve in cases where UAV is suspected.
单叶主动脉瓣(UAV)是一种罕见的先天性异常,通常影响四五十岁的患者,并伴有心力衰竭的症状。我们的病例是一名此前无症状的患有单叶主动脉瓣的少女,她出现心脏骤停并得到了成功治疗。文献中仅报道了另外两例类似病例,均为年龄稍大的男性患者。我们的病例突出了与该异常相关的发病率,支持在怀疑单叶主动脉瓣的病例中对瓣膜进行仔细评估的必要性。