Karimi Mohsen, Kirshbom Paul M, Kopf Gary S, Steele Margaret M, Sullivan Jill M
Department of Surgery, Section of Cardiac Surgery, Pediatric Cardiothoracic Surgery, Northeast Pediatric Specialties (NEPS), Yale University School of Medicine, New Haven, CT, USA Connecticut Children's Medical Center, Hartford, CT, USA
Department of Surgery, Section of Cardiac Surgery, Pediatric Cardiothoracic Surgery, Northeast Pediatric Specialties (NEPS), Yale University School of Medicine, New Haven, CT, USA Connecticut Children's Medical Center, Hartford, CT, USA.
World J Pediatr Congenit Heart Surg. 2015 Jul;6(3):462-5. doi: 10.1177/2150135114558848.
Transposition of the great arteries (TGA) with intact ventricular septum (IVS) has very favorable short- and long-term surgical outcome. Although rare, when associated with persistent pulmonary hypertension (PPH), it exhibits significant mortality risk and management challenges. We report the case of a neonate with TGA with IVS and PPH who underwent successful early surgical repair with emphasis on clinical management and review of the literature.
室间隔完整的大动脉转位(TGA)具有非常良好的短期和长期手术效果。虽然罕见,但当与持续性肺动脉高压(PPH)相关时,它会呈现出显著的死亡风险和管理挑战。我们报告了一例患有室间隔完整的TGA和PPH的新生儿病例,该患儿接受了成功地早期手术修复,并重点阐述了临床管理及文献回顾。