Bielowicz-Hilgier A
Probl Med Wieku Rozwoj. 1979;9:177-208.
The research investigations carried out for years revealed most details on embryology nd pathophysiology of anorectal malformations. They left still unsolved the problem how to obtain better functional results following their surgical treatment. It is well known, that in the group of high- supralevator deformities, the lower rectum, anal canal and internal sphincter are absent, and the terminal pouch lyes above the puborectalis sling. The purpose of the of the pull-through procedure is the reconstruction of proper relationship between bowel, the levator diaphragm and external sphincter, without damage to the muscles and pelvic plexus. The technics advocated by Stephens and Rehbein are apparently important steps forward in surgery of these defects. The sacrococcygeal route of Kraske, adapted by Stephens for operative treatment of anorectal malformations, gives approach from behind to the supralevator space for identification of puborectalis sling. The muscle is separated from urethra or vagina, and gradually the tunnel through the sling and external sphincter is created. The gentle and in proper plane pull of the bowel through an undamaged puborectalis muscle gives the possibility to save its function as rectal sphincter and receptor as well. This paper presents 76 children with anorectal malformations, treated in the Department of Pediatric Surgery during 1966 to 1975 yr. The "International" Classification, proposed in Melbourne was used to group the patients according to the level of the terminal bowel: in Supralevator , Intermediate and Translevator defects (tab. I-III). The surgical procedures in particular types of anomalies are presented in the tables IV-VII. The detailed clinical evaluation and roentgenological examination were the base to assess the type of malformation and to choose the method of treatment. To find other coincidental malformations, generally most frequently occurring in the genitourinary tract, the intravenous pyelography was the routine early investigation. Other tests, like cystography and endoscopy were done when indicted. The genitourinary tract abnormalities were found in 9 of 14 children with supralevator deformities, in 9 of 17 children with intermediate type and in 17 of 45 from the translevator group. Oesophageal atresia was present in 6 children, the congenital heart failure in 13 and skeletal malformations in 21 of the total. In neonates with supralevator anomalies the primary reconstructions were not very successful, so transversostomy became a routine preliminary procedure.(ABSTRACT TRUNCATED AT 400 WORDS)
多年来开展的研究调查揭示了肛门直肠畸形胚胎学和病理生理学的大部分细节。但在其手术治疗后如何获得更好的功能结果这一问题上仍未解决。众所周知,在高位(肛提肌上)畸形组中,低位直肠、肛管和内括约肌缺失,终末袋位于耻骨直肠肌吊带上方。拖出术的目的是重建肠管、肛提肌膈和外括约肌之间的正常关系,同时不损伤肌肉和盆腔神经丛。斯蒂芬斯(Stephens)和雷布欣(Rehbein)倡导的技术显然是这些缺陷手术治疗方面向前迈出的重要一步。克拉斯克(Kraske)的骶尾途径经斯蒂芬斯改编用于肛门直肠畸形的手术治疗,可从后方进入肛提肌上间隙以识别耻骨直肠肌吊带。将该肌肉与尿道或阴道分离,然后逐渐在吊带和外括约肌中创建隧道。轻柔且在合适平面将肠管通过未受损的耻骨直肠肌牵拉,有可能保留其作为直肠括约肌和感受器的功能。本文介绍了1966年至1975年期间在小儿外科治疗的76例肛门直肠畸形患儿。采用在墨尔本提出的“国际”分类法,根据终末肠管的水平对患者进行分组:高位(肛提肌上)、中间型和经肛提肌型缺陷(表I - III)。特定类型异常的手术方法见表IV - VII。详细的临床评估和放射学检查是评估畸形类型和选择治疗方法的基础。为发现其他合并畸形,通常最常见于泌尿生殖道,静脉肾盂造影是常规的早期检查。当有指征时进行其他检查,如膀胱造影和内镜检查。在14例高位畸形患儿中有9例发现泌尿生殖道异常,17例中间型患儿中有9例,经肛提肌组45例中有17例。总共6例患儿存在食管闭锁,13例有先天性心力衰竭,21例有骨骼畸形。在高位畸形的新生儿中,一期重建不太成功,因此横结肠造口术成为常规的初步手术。(摘要截断于400字)