Matsuzono Tomoko, Chan Cyrus Yin-Ho, Chan May Yuk-May
Department of Obstetrics and Gynaecology, Queen Elizabeth Hospital, Hong Kong, China;
Department of Radiology, Queen Elizabeth Hospital, Hong Kong, China.
Intractable Rare Dis Res. 2015 Aug;4(3):152-4. doi: 10.5582/irdr.2015.01016.
A 56 year old postmenopausal lady presented with a rapidly enlarging pelvis mass. Clinical and ultrasonographic features were compatible with a rapidly enlarging fibroid with possible sarcomatous changes, and hence, computated tomography (CT) scan was performed to further delineate the nature and extent of the disease. However, CT scan revealed a huge tumour arising from the retroperitoneal space along the course of the left gonadal vein with typical radiological features of a gonadal vein leiomyosarcoma which were described in previous literatures. With joint collaboration with the surgeons, radical surgery with optimal debulking was subsequently performed for the patient and the diagnosis was confirmed intra-operatively and histologically.
一位56岁的绝经后女性因盆腔肿物迅速增大前来就诊。临床及超声检查结果提示可能为快速增大的肌瘤并伴有肉瘤样变,因此,行计算机断层扫描(CT)以进一步明确病变的性质及范围。然而,CT扫描显示一个巨大肿瘤起源于沿左侧性腺静脉走行的腹膜后间隙,具有性腺静脉平滑肌肉瘤典型的影像学特征,此前文献已有描述。随后,在外科医生的共同协作下,为患者实施了根治性手术及最佳减瘤手术,术中及组织学检查均证实了诊断。