Bass Annatina, Husner Alexander, Metternich Frank
1 HNO-Klinik, Universitätsspital Basel.
2 Klinik für HNO, Hals- und Gesichtschirurgie, Kantonsspital Aarau.
Praxis (Bern 1994). 2015 Sep 30;104(20):1097-9. doi: 10.1024/1661-8157/a002159.
Malignant peripheral nerve sheath tumors (MPNST) are rare. But especially in patients with known neurofibromatosis type 1 (von Recklinghausen), this entity of tumors should not be forgotten. The indication for open biopsy or excision should be made generously. In the following, we report a rare case of MPNST, which highlights the importance of rapid diagnosis and treatment.
恶性外周神经鞘瘤(MPNST)较为罕见。但尤其对于已知患有1型神经纤维瘤病(冯雷克林霍增氏病)的患者,这类肿瘤不应被忽视。对于开放性活检或切除的指征应放宽掌握。在此,我们报告一例罕见的MPNST病例,该病例凸显了快速诊断和治疗的重要性。