[血管肉瘤酷似复发性肺栓塞]
[Angiosarcoma mimicking recurrent pulmonary embolism].
作者信息
Goyard C, Sanchez O, Mourin G, Mussot S, Boudjemaa A, de Montpreville V, Meyer G, Ferre A
机构信息
Service de pneumologie et soins intensifs, hôpital européen Georges-Pompidou, 75015 Paris, France.
Service de pneumologie et soins intensifs, hôpital européen Georges-Pompidou, 75015 Paris, France; Université Paris Descartes, Sorbonne Paris Cité, 75006 Paris, France.
出版信息
Rev Mal Respir. 2016 May;33(5):377-82. doi: 10.1016/j.rmr.2015.07.001. Epub 2015 Oct 24.
INTRODUCTION
Pulmonary artery sarcoma is a rare disease with non-specific symptoms. The clinical and radiological presentation can mimic pulmonary embolism with chronic thromboembolic pulmonary hypertension. Management is essentially surgical but the prognosis remains poor.
CASE REPORT
A patient presented with symptoms of pulmonary embolism. Despite vitamin K antagonist therapy, he suffered from extension of the endovascular defects and his pulmonary hypertension increased. Suspicious results of positron emission tomography suggested the diagnosis of pulmonary artery sarcoma that was confirmed by surgery. However, the outcome was unfavourable, leading to death of the patient.
CONCLUSION
This case reinforces the idea that the clinical and tomodensitometric presentations of pulmonary arterial sarcoma and chronic thromboembolic pulmonary hypertension are similar. The positron emission tomography seems to be a key to distinguishing these two diagnoses.
引言
肺动脉肉瘤是一种症状不具特异性的罕见疾病。其临床和放射学表现可类似于伴有慢性血栓栓塞性肺动脉高压的肺栓塞。治疗主要为手术治疗，但预后仍然很差。
病例报告
一名患者出现肺栓塞症状。尽管接受了维生素K拮抗剂治疗，但他的血管内缺损仍有进展，肺动脉高压加重。正电子发射断层扫描的可疑结果提示肺动脉肉瘤的诊断，手术证实了这一诊断。然而，结果并不理想，导致患者死亡。
结论
该病例强化了肺动脉肉瘤与慢性血栓栓塞性肺动脉高压的临床和体层摄影表现相似的观点。正电子发射断层扫描似乎是区分这两种诊断的关键。
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