Ishii Yoichiro, Miyamoto Takashi, Nakajima Kimiko, Tanaka Kensuke, Ikeda Kentaro, Inamura Noboru, Takagi Takeshi, Kobayashi Tomio, Arakawa Hirokazu
Department of Cardiology, Gunma Children's Medical Center, Gunma, Japan.
Department of Pediatrics, Gunma University Graduate School of Medicine, Gunma, Japan.
Pediatr Int. 2016 Feb;58(2):158-61. doi: 10.1111/ped.12744. Epub 2015 Nov 26.
Left pulmonary artery sling (LPAS) is a rare vascular anomaly. The left pulmonary artery arises distally from the right pulmonary artery on the right side of the trachea and passes between the trachea and esophagus towards the left lung, compressing the lower trachea. LPAS is associated with congenital tracheal stenosis, which frequently requires early surgical intervention and has a poor prognosis due to severe airway obstruction after birth. Therefore, LPAS should be prenatally diagnosed to prepare for surgical intervention for tracheal stenosis. To the best of our knowledge, there are few reports on prenatal echocardiographic findings in LPAS. We report three prenatal cases of LPAS, which resulted in respiratory symptoms. We discuss fetal ultrasound findings and highlight the abnormal rotation of the fetal cardiac axis to the right as a useful sign in the prenatal screening of LPAS.
左肺动脉吊带(LPAS)是一种罕见的血管异常。左肺动脉在气管右侧从右肺动脉远端发出,在气管和食管之间向左肺走行,压迫气管下段。LPAS与先天性气管狭窄相关,后者常需要早期手术干预,且由于出生后严重气道梗阻,预后较差。因此,应在产前诊断LPAS,为气管狭窄的手术干预做准备。据我们所知,关于LPAS产前超声心动图表现的报道较少。我们报告3例导致呼吸症状的LPAS产前病例。我们讨论胎儿超声检查结果,并强调胎儿心轴向右异常旋转作为LPAS产前筛查的一个有用征象。