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累及腰神经根并附着终丝的髓外圆锥室管膜瘤

Extramedullary Conus Ependymoma Involving a Lumbar Nerve Root with Filum Terminale Attachment.

作者信息

Moriwaki Takashi, Iwatsuki Koichi, Ohnishi Yu-Ichiro, Ninomiya Koshi, Yoshimine Toshiki

机构信息

Department of Neurosurgery, Osaka University Graduate School of Medicine, Osaka, Japan.

出版信息

Clin Med Insights Case Rep. 2015 Nov 30;8:101-4. doi: 10.4137/CCRep.S24719. eCollection 2015.

Abstract

PURPOSE

In the current report, we describe a case of an extramedullary ependymoma involving a lumbar nerve root near conus medullaris. Spinal ependymomas commonly present as intramedullary tumors in the cervical or thoracic cord or as tumors arising from the conus medullaris or the filum terminale. In this case, we showed an extramedullary conus ependymoma involving a lumbar nerve root with filum terminale attachment.

CASE PRESENTATION

A 69-year-old woman presented with lower back pain, but without sensory disturbance or motor weakness in her lower extremities.

CLINICAL ASSESSMENT

Magnetic resonance imaging revealed an intradural mass at T12-L1 at the conus medullaris, which was totally resected. Histopathology revealed a non-myxopapillary ependymoma (WHO grade 2). Postoperatively, the patient did well and displayed no neurological deficits. Moreover, no radiotherapy was required.

CONCLUSIONS

This report documented a rare case of intradural extramedullary ependymoma located at the conus medullaris, involving the lumbar nerve root, and attached to the filum terminale. Although extramedullary ependymomas at this region are more frequently classified as myxopapillary, histopathological examination revealed this tumor as a non-myxopapillary ependymoma.

摘要

目的

在本报告中,我们描述了一例髓外室管膜瘤,累及脊髓圆锥附近的腰神经根。脊髓室管膜瘤通常表现为颈段或胸段脊髓内的肿瘤,或起源于脊髓圆锥或终丝的肿瘤。在本病例中,我们展示了一例累及腰神经根并附着于终丝的髓外圆锥室管膜瘤。

病例介绍

一名69岁女性因下背部疼痛就诊,但下肢无感觉障碍或运动无力。

临床评估

磁共振成像显示脊髓圆锥T12-L1水平硬膜内有一肿块,已全部切除。组织病理学显示为非黏液乳头型室管膜瘤(世界卫生组织2级)。术后,患者恢复良好,无神经功能缺损。此外,无需放疗。

结论

本报告记录了一例罕见的位于脊髓圆锥的硬膜内髓外室管膜瘤,累及腰神经根并附着于终丝。尽管该区域的髓外室管膜瘤更常被归类为黏液乳头型,但组织病理学检查显示该肿瘤为非黏液乳头型室管膜瘤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ec1f/4666522/11aa6a28a1e4/ccrep-8-2015-101f1.jpg

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