Lv Yan, Pang Xin, Zhang Qingfu, Jia Dalin
Department of Cardiovascular, The First Affiliated Hospital of China Medical University Shenyang 110001, People's Republic of China.
Department of Cardiac Surgery, The First Affiliated Hospital of China Medical University Shenyang 110001, People's Republic of China.
Int J Clin Exp Pathol. 2015 Nov 1;8(11):15412-6. eCollection 2015.
Leiomyosarcoma of the heart is extremely rare and may involve many symptoms. The outcome is poor and the median survival is only 6 months.
A 43-years-old female patient complained of palpitation and dyspnea and was diagnosed as bilateral iliac vein-inferior vena cava-right atrium-pulmonary masses. Pathological diagnosis was leiomyosarcoma of vascular origin and she survived for 12 months after surgery.
According to the summarization of 30 vascular leiomyosarcoma cases with heart involved we can find that surgical resection is the basic treatment for cardiac leiomyosarcoma, and surgery combined with chemotherapy may be able to further prolong survival.
心脏平滑肌肉瘤极为罕见,可能出现多种症状。预后较差,中位生存期仅6个月。
一名43岁女性患者主诉心悸和呼吸困难,被诊断为双侧髂静脉-下腔静脉-右心房-肺部肿块。病理诊断为血管源性平滑肌肉瘤,术后存活12个月。
通过对30例累及心脏的血管平滑肌肉瘤病例总结发现,手术切除是心脏平滑肌肉瘤的基本治疗方法,手术联合化疗可能进一步延长生存期。