人工耳蜗植入是患有感音神经性听力损失的浅表性铁沉积症患者的一种治疗选择。
Cochlear implantation is a therapeutic option for superficial siderosis patients with sensorineural hearing loss.
作者信息
Omichi R, Kariya S, Maeda Y, Nishizaki K
机构信息
Department of Otolaryngology - Head and Neck Surgery,Graduate School of Medicine,Dentistry and Pharmaceutical Sciences,Okayama University,Japan.
出版信息
J Laryngol Otol. 2016 Apr;130(4):408-11. doi: 10.1017/S0022215116000335. Epub 2016 Feb 9.
BACKGROUND
Superficial siderosis is a rare disease that results from chronic bleeding in the subarachnoid space. Haemosiderin deposits throughout the subpial layers of the brain and spinal cord lead to progressive sensorineural hearing loss, which is seen in 95 per cent of patients with superficial siderosis. The impact of cochlear implantation on the quality of life of superficial siderosis patients is under debate.
CASE REPORT
A 38-year-old male with superficial siderosis presented with bilateral progressive sensorineural hearing loss. The patient underwent cochlear implantation and his quality of life was improved as evaluated by the Abbreviated Profile of Hearing Aid Benefit inventory.
CONCLUSION
The remarkable improvement in Abbreviated Profile of Hearing Aid Benefit scores shown in this study indicates that cochlear implantation leads to a better quality of life in superficial siderosis patients.
背景
表面性铁沉积症是一种由蛛网膜下腔慢性出血导致的罕见疾病。含铁血黄素沉积于脑和脊髓软膜下各层，会导致进行性感音神经性听力损失，95%的表面性铁沉积症患者会出现这种情况。人工耳蜗植入对表面性铁沉积症患者生活质量的影响存在争议。
病例报告
一名38岁患有表面性铁沉积症的男性出现双侧进行性感音神经性听力损失。该患者接受了人工耳蜗植入，通过助听器效益简表评估，其生活质量得到了改善。
结论
本研究中助听器效益简表得分的显著改善表明，人工耳蜗植入可使表面性铁沉积症患者的生活质量更好。
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