一名年轻成人发生内膜中层黏液样变性，导致主动脉和肾动脉瘤。
Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult.
作者信息
Viljoen Charle, Szymanski Patryk, Osman Naeem, Henning Kristin Lorenc, Scholtz Paul, Rayner Brian, Naidoo Nadraj
机构信息
Department of Medicine, Groote Schuur Hospital and University of Cape Town, South Africa.
Division of Anatomical Pathology, National Health Laboratory Service, Groote Schuur Hospital and University of Cape Town, South Africa.
出版信息
Cardiovasc J Afr. 2016 Jan-Feb;27(1):49-52. doi: 10.5830/CVJA-2015-079.
Intimomedial mucoid degeneration (IMMD) is characterised by aneurysm formation following mucin deposition in the intima and media, with elastic tissue degeneration of the arterial wall. We present a case of a young adult who developed a diffusely aneurysmal aorta and its major branches, which was histopathologically confirmed as intimomedial mucoid degeneration, and a review of the literature. This case report attempts to raise the awareness of the reader to this rare cause of aortic aneurysm and to the bleeding diathesis associated with IMMD that may complicate surgery.
内膜中层黏液样变性（IMMD）的特征是在内膜和中膜黏蛋白沉积后形成动脉瘤，伴有动脉壁弹性组织变性。我们报告一例年轻成人病例，其主动脉及其主要分支出现弥漫性动脉瘤，经组织病理学证实为内膜中层黏液样变性，并对相关文献进行综述。本病例报告旨在提高读者对这种罕见的主动脉瘤病因以及与IMMD相关的、可能使手术复杂化的出血素质的认识。
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