Gong Yubao, Yang Chen, Liu Yang, Liu Jianguo, Qi Xin
Department of Bone and Joint Surgery, The First Hospital of Jilin University, Changchun, Jilin 130021, P.R. China.
Department of Radiology, The First Hospital of Jilin University, Changchun, Jilin 130021, P.R. China.
Exp Ther Med. 2016 Jun;11(6):2361-2364. doi: 10.3892/etm.2016.3180. Epub 2016 Mar 23.
Hereditary onycho-osteodysplasia, also known as nail-patella syndrome (NPS), is a rare genetic disorder that is primarily characterized by poorly developed nails and patella. Patients with NPS frequently suffer from patellar instability that requires surgical management. The present case report describes a 25-year-old man with NPS. The patient presented with left knee pain and was found to have recurrent left patellar dislocation. The knee pain was first reported 1-year after a minor knee trauma incident. Following complete evaluation, a diagnosis of NPS was reached. The patient underwent surgical intervention using medial patellofemoral ligament (MPFL) reconstruction with a gracilis tendon autograft looped through two transverse 3.2-mm drill holes in the patella and fixed at the natural MPFL insertion site on the medial femoral condyle with an interference screw. The surgery resulted in stabilization of the patella in the femoral trochlea and the patient did not have any subsequent dislocations or subluxations. The patient had an excellent range of knee movement in the follow-up period. This case indicates that MPFL reconstruction in patients with patellar dislocation secondary to NPS can successfully restore normal patellar tracking and result in good range of movement and functional activity.
遗传性甲髌发育不良,也称为指甲-髌骨综合征(NPS),是一种罕见的遗传性疾病,主要特征是指甲和髌骨发育不良。NPS患者经常遭受髌骨不稳定,需要手术治疗。本病例报告描述了一名25岁的NPS男性患者。该患者因左膝疼痛就诊,被发现有复发性左髌骨脱位。膝痛首次报告于一次轻微膝部外伤事件后1年。经过全面评估,确诊为NPS。患者接受了手术干预,采用内侧髌股韧带(MPFL)重建术,取自体股薄肌腱,穿过髌骨上两个3.2毫米的横向钻孔,并通过一枚挤压螺钉固定在股骨内侧髁的MPFL自然附着部位。手术使髌骨在股骨滑车中稳定,患者随后未再发生脱位或半脱位。在随访期间,患者膝关节活动范围良好。该病例表明,对于NPS继发髌骨脱位的患者,MPFL重建术可成功恢复正常髌骨轨迹,并产生良好的活动范围和功能活动。