囊性纤维化中的气胸：超越指南

Pneumothorax in cystic fibrosis: beyond the guidelines.

作者信息

Lord Robert W, Jones Andrew M, Webb A Kevin, Barry Peter J

机构信息

Manchester Adult Cystic Fibrosis Centre, University Hospital of South Manchester, Southmoor Road, Wythenshawe, M23 9LT, United Kingdom; Institute of Inflammation and Repair, University of Manchester, United Kingdom.

出版信息

Paediatr Respir Rev. 2016 Aug;20 Suppl:30-3. doi: 10.1016/j.prrv.2016.06.012. Epub 2016 Jun 15.

DOI:10.1016/j.prrv.2016.06.012

PMID:27374621

Abstract

Pneumothorax is a serious but common complication in patients with cystic fibrosis (CF). It has adverse prognostic implications as well as associations with subsequent reduction in lung function and significant risk of recurrence. Management dilemmas frequently occur that are beyond current guidelines. We review the evidence and highlight management difficulties in pneumothoraces in CF.

摘要

气胸是囊性纤维化（CF）患者中一种严重但常见的并发症。它具有不良的预后影响，还与随后的肺功能下降以及显著的复发风险相关。经常会出现超出当前指南范畴的管理难题。我们回顾相关证据，并着重指出CF患者气胸的管理难点。