Hamaya K, Kitamura M, Doi K
Anatomic Pathology, Surgery, Okayama Saiseikai General Hospital, Japan.
Acta Pathol Jpn. 1989 Mar;39(3):207-11. doi: 10.1111/j.1440-1827.1989.tb01502.x.
The proximal jejunum, containing four separate amyloid tumors, was resected from a chronically constipated 71-year-old male exhibiting IgG lambda monoclonal gammopathy. Amyloid was deposited in the jejunal wall, mesentery and regional lymph nodes, but was not seen in gastric and rectal biopsy samples. Two years after surgery, the patient is well, but the monoclonal gammopathy persists.
从一名患有慢性便秘的71岁男性身上切除了含有四个独立淀粉样瘤的空肠近端,该男性表现出IgG λ单克隆丙种球蛋白病。淀粉样蛋白沉积在空肠壁、肠系膜和区域淋巴结中,但在胃和直肠活检样本中未发现。手术后两年,患者情况良好,但单克隆丙种球蛋白病仍然存在。