Orvain C, Luque Paz D, Dobo I, Cottin L, Le Calvez G, Chauveau A, Mercier M, Farhi J, Boyer F, Ianotto J C, Guibourg B, Rousselet M C, Zandecki M, Ifrah N, Hunault-Berger M, Ugo V, Genevieve F
Service des Maladies du Sang, CHU d'Angers, Angers, France.
Laboratoire d'Hématologie, CHU d'Angers, Angers, France.
Ann Hematol. 2016 Oct;95(11):1819-23. doi: 10.1007/s00277-016-2784-x. Epub 2016 Sep 1.
A high number of circulating CD34+ cells has been advocated to distinguish primary myelofibrosis from other Philadelphia-negative myeloproliferative neoplasms. We re-evaluated the diagnostic interest of measuring circulating CD34+ cells in 26 healthy volunteers and 256 consecutive patients at diagnosis for whom a myeloproliferative neoplasm was suspected. The ROC curve analysis showed that a number of CD34+ <10/μl excludes the diagnosis of primary myelofibrosis with a sensitivity of 97 % and a specificity of 90 % (area under the curve: 0.93 [0.89-0.98]; p < 0.001). Patients with PMF harboring a CALR mutation had more circulating CD34+ cells than patients with either a JAK 2 or MPL mutation (p = 0.02 and p < 0.01, respectively). These results suggest that this fast, simple, non-invasive, and standardized test is of particular interest to exclude the diagnosis of primary myelofibrosis.
大量循环CD34+细胞被认为可用于区分原发性骨髓纤维化与其他费城染色体阴性的骨髓增殖性肿瘤。我们重新评估了测量循环CD34+细胞在26名健康志愿者和256例连续诊断时疑似骨髓增殖性肿瘤患者中的诊断价值。ROC曲线分析显示,CD34+细胞数<10/μl可排除原发性骨髓纤维化的诊断,敏感性为97%,特异性为90%(曲线下面积:0.93[0.89 - 0.98];p<0.001)。携带CALR突变的原发性骨髓纤维化患者比携带JAK 2或MPL突变的患者循环CD34+细胞更多(分别为p = 0.02和p<0.01)。这些结果表明,这种快速、简单、无创且标准化的检测对于排除原发性骨髓纤维化的诊断具有特别的意义。