Treitl Daniela, Roudenko Alexandra, El Hussein Siba, Rizer Magda, Bao Philip
Mount Sinai Medical Center, 4300 Alton Road, Miami Beach, FL 33140, USA.
Mount Sinai West, 1000 10th Avenue, New York, NY 10019, USA.
Case Rep Surg. 2016;2016:5625762. doi: 10.1155/2016/5625762. Epub 2016 Nov 8.
Undifferentiated embryonal sarcomas of the liver are extremely rare cases in adults. We report the case of a 30-year-old male who presented with early satiety and abdominal pain due to a massive tumor originating from the left liver and occupying the entire epigastrium. The patient underwent bland embolization in an attempt to decrease the size of the tumor. He then underwent a formal left hepatectomy with resection of liver segments 2, 3, and 4. Extrahepatic inflow control of the portal vein and hepatic artery was performed prior to parenchymal transection. No Pringle maneuver was required. Pathology analysis showed a 45 cm tumor consistent with an undifferentiated embryonal sarcoma and negative microscopic margins. The epidemiology, treatment, and prognosis of this unusual cancer presentation are reviewed.
肝未分化胚胎性肉瘤在成人中极为罕见。我们报告一例30岁男性病例,该患者因起源于左肝的巨大肿瘤占据整个上腹部而出现早饱感和腹痛。患者接受了单纯栓塞术以试图缩小肿瘤大小。随后他接受了正式的左肝切除术,切除了肝段2、3和4。在实质切开之前对门静脉和肝动脉进行了肝外血流控制。无需进行普林格尔手法。病理分析显示一个45厘米的肿瘤,符合未分化胚胎性肉瘤,显微镜下切缘阴性。本文对这种不寻常癌症表现的流行病学、治疗和预后进行了综述。