Mattioni Laura, Peña María Elena, Ringa Maximiliano, Schlottmann Francisco, Bugari Gustavo
Servicio de Cirugía General, Departamento de Cirugía, Hospital Alemán de Buenos Aires, Argentina.
Servicio de Cirugía General, Departamento de Cirugía, Hospital Alemán de Buenos Aires, Argentina. E-mail:
Medicina (B Aires). 2017;77(1):43-45.
Wandering spleen syndrome is a rare condition in which absence or laxity of splenic fixing elements predisposes to an unusual location in the abdomen and an increasing risk of twisting and infarction. Its etiology may be congenital or acquired and clinical presentation is variable. Diagnosis is based on clinical suspicion, laboratory and imaging. Surgery is the only definitive treatment for this pathology. We report the case of a 23 year old woman with a history of recurrent episodes of abdominal pain in the left upper quadrant since childhood. On physical examination she was afebrile, hemodynamically stable, with marked abdominal tenderness in the left upper quadrant. Ultrasonography showed homogeneous splenomegaly. Abdominal CT-scan presented an enlarged, eutopic spleen, with swirling and congestion of hilum vessels. Splenic ischemia due to organ torsion was suspected. Exploratory laparoscopy was performed showing an 18 cm in diameter spleen free in left upper quadrant, with varicose veins in the periphery and without fixing ligaments. Laparoscopic splenectomy was completed. The pathology report showed ischemic necrosis of the organ. The patient progressed favorably and was discharged on the third postoperative day.
游走脾综合征是一种罕见病症,其中脾固定结构的缺失或松弛会导致脾脏在腹腔内位置异常,并增加扭转和梗死的风险。其病因可能是先天性的或后天获得性的,临床表现多样。诊断基于临床怀疑、实验室检查和影像学检查。手术是治疗这种病症的唯一确切方法。我们报告一例23岁女性病例,该患者自童年起就有左上腹反复腹痛发作史。体格检查时,她体温正常,血流动力学稳定,左上腹有明显压痛。超声检查显示脾脏均匀肿大。腹部CT扫描显示脾脏增大,位置正常,但脾门血管有扭曲和充血。怀疑是器官扭转导致脾缺血。进行了 exploratory laparoscopy(此处原文有误,推测应为“探查性腹腔镜检查”),结果显示左上腹有一个直径18厘米的游离脾脏,周边有静脉曲张且无固定韧带。完成了腹腔镜脾切除术。病理报告显示该器官有缺血性坏死。患者恢复良好,术后第三天出院。