Monast C S, Li K, Judson M A, Baughman R P, Wadman E, Watt R, Silkoff P E, Barnathan E S, Brodmerkel C
Janssen Research & Development, LLC, Spring House, PA, USA.
Albany Medical College, Albany, NY, USA.
Clin Exp Immunol. 2017 Jun;188(3):444-454. doi: 10.1111/cei.12942. Epub 2017 Mar 27.
The molecular basis of sarcoidosis phenotype heterogeneity and its relationship to effective treatment of sarcoidosis have not been elucidated. Peripheral samples from sarcoidosis subjects who participated in a Phase II study of golimumab [anti-tumour necrosis factor (TNF)-α] and ustekinumab [anti-interleukin (IL)-12p40] were used to measure the whole blood transcriptome and levels of serum proteins. Differential gene and protein expression analyses were used to explore the molecular differences between sarcoidosis phenotypes as defined by extent of organ involvement. The same data were also used in conjunction with an enrichment algorithm to identify gene expression changes associated with treatment with study drugs compared to placebo. Our analyses revealed marked heterogeneity among the three sarcoidosis phenotypes included in the study cohort, including striking differences in enrichment of the interferon pathway. Conversely, enrichments of multiple pathways, including T cell receptor signalling, were similar among phenotypes. We also identify differences between treatment with golimumab and ustekinumab that may explain the differences in trends for clinical efficacy observed in the trial. We find that molecular heterogeneity is associated with sarcoidosis in a manner that may be related to the extent of organ involvement. These findings may help to explain the difficulty in identifying clinically efficacious sarcoidosis treatments and suggest hypotheses for improved therapeutic strategies.
结节病表型异质性的分子基础及其与结节病有效治疗的关系尚未阐明。来自参与戈利木单抗[抗肿瘤坏死因子(TNF)-α]和优特克单抗[抗白细胞介素(IL)-12p40]II期研究的结节病受试者的外周样本用于测量全血转录组和血清蛋白水平。采用差异基因和蛋白质表达分析来探索由器官受累程度定义的结节病表型之间的分子差异。相同的数据还与富集算法结合使用,以识别与使用研究药物治疗相比安慰剂治疗相关的基因表达变化。我们的分析揭示了研究队列中纳入的三种结节病表型之间存在明显的异质性,包括干扰素途径富集方面的显著差异。相反,多种途径的富集,包括T细胞受体信号传导,在各表型之间是相似的。我们还确定了戈利木单抗和优特克单抗治疗之间的差异,这可能解释了试验中观察到的临床疗效趋势差异。我们发现分子异质性与结节病相关,其方式可能与器官受累程度有关。这些发现可能有助于解释确定结节病临床有效治疗方法的困难,并为改进治疗策略提出假设。