Smith-Hicks Constance L, Cai Peiling, Savonenko Alena V, Reeves Roger H, Worley Paul F
Solomon H. Snyder Department of Neuroscience, Johns Hopkins University School of MedicineBaltimore, MD, USA; Department of Neurology, Johns Hopkins University School of MedicineBaltimore, MD, USA.
The State Key Laboratory of Biotherapy, West-China Hospital, Sichuan University Chengdu, China.
Front Neural Circuits. 2017 Feb 3;11:6. doi: 10.3389/fncir.2017.00006. eCollection 2017.
Down syndrome (DS) is the leading chromosomal cause of intellectual disability, yet the neural substrates of learning and memory deficits remain poorly understood. Here, we interrogate neural networks linked to learning and memory in a well-characterized model of DS, the Ts65Dn mouse. We report that Ts65Dn mice exhibit exploratory behavior that is not different from littermate wild-type (WT) controls yet behavioral activation of Arc mRNA transcription in pyramidal neurons of the CA1 region of the hippocampus is altered in Ts65Dn mice. In WT mice, a 5 min period of exploration of a novel environment resulted in Arc mRNA transcription in 39% of CA1 neurons. By contrast, the same period of exploration resulted in only ~20% of CA1 neurons transcribing Arc mRNA in Ts65Dn mice indicating increased sparsity of the behaviorally induced ensemble. Like WT mice the CA1 pyramidal neurons of Ts65Dn mice reactivated Arc transcription during a second exposure to the same environment 20 min after the first experience, but the size of the reactivated ensemble was only ~60% of that in WT mice. After repeated daily exposures there was a further decline in the size of the reactivated ensemble in Ts65Dn and a disruption of reactivation. Together these data demonstrate reduction in the size of the behaviorally induced network that expresses Arc in Ts65Dn mice and disruption of the long-term stability of the ensemble. We propose that these deficits in network formation and stability contribute to cognitive symptoms in DS.
唐氏综合征(DS)是导致智力残疾的主要染色体病因,然而学习和记忆缺陷的神经基础仍知之甚少。在此,我们在一个特征明确的DS模型——Ts65Dn小鼠中,研究与学习和记忆相关的神经网络。我们报告称,Ts65Dn小鼠表现出的探索行为与同窝野生型(WT)对照并无差异,但Ts65Dn小鼠海马体CA1区锥体神经元中Arc mRNA转录的行为激活发生了改变。在WT小鼠中,5分钟的新环境探索导致39%的CA1神经元转录Arc mRNA。相比之下,相同时间段的探索在Ts65Dn小鼠中仅导致约20%的CA1神经元转录Arc mRNA,这表明行为诱导的神经元集群的稀疏性增加。与WT小鼠一样,Ts65Dn小鼠的CA1锥体神经元在首次经历20分钟后再次暴露于相同环境时重新激活了Arc转录,但重新激活集群的大小仅为WT小鼠的约60%。经过每日重复暴露后,Ts65Dn小鼠中重新激活集群的大小进一步下降,且重新激活受到破坏。这些数据共同表明,Ts65Dn小鼠中表达Arc的行为诱导网络的大小减小,且神经元集群的长期稳定性受到破坏。我们认为,这些网络形成和稳定性方面的缺陷导致了DS的认知症状。