原发性纤毛运动障碍患者的高渗盐水：迈向罕见肺部疾病循证治疗之路 - Suppr

Suppr

超能文献

Hypertonic saline in patients with primary ciliary dyskinesia: on the road to evidence-based treatment for a rare lung disease.

作者信息

Kuehni Claudia E, Goutaki Myrofora, Kobbernagel Helene E

机构信息

Institute of Social and Preventive Medicine, University of Bern, Switzerland

Paediatric Respiratory Medicine, Children's University Hospital of Bern, University of Bern, Switzerland.

出版信息

Eur Respir J. 2017 Feb 23;49(2). doi: 10.1183/13993003.02514-2016. Print 2017 Feb.

DOI:10.1183/13993003.02514-2016

PMID:28232418

Abstract

摘要

相似文献

Hypertonic saline in patients with primary ciliary dyskinesia: on the road to evidence-based treatment for a rare lung disease.

Eur Respir J. 2017 Feb 23;49(2). doi: 10.1183/13993003.02514-2016. Print 2017 Feb.

Rapid Advances in Primary Ciliary Dyskinesia Research. A Brief Update for Pulmonologists.

Am J Respir Crit Care Med. 2019 Jan 15;199(2):136-138. doi: 10.1164/rccm.201807-1390ED.

Outcomes of lung transplantation for primary ciliary dyskinesia and Kartagener syndrome.

J Heart Lung Transplant. 2016 Nov;35(11):1377-1378. doi: 10.1016/j.healun.2016.08.025. Epub 2016 Sep 7.

A randomised controlled trial on the effect of inhaled hypertonic saline on quality of life in primary ciliary dyskinesia.

Eur Respir J. 2017 Feb 23;49(2). doi: 10.1183/13993003.01770-2016. Print 2017 Feb.

Primary ciliary dyskinesia: keep it on your radar.

Thorax. 2018 Feb;73(2):101-102. doi: 10.1136/thoraxjnl-2017-210776. Epub 2017 Nov 13.

Lung function in primary ciliary dyskinesia: breaking the myth that this is a mild disease.

Eur Respir J. 2018 Aug 23;52(2). doi: 10.1183/13993003.01365-2018. Print 2018 Aug.

[Primary ciliary dyskinesia, immotile cilia syndrome, and Kartagener syndrome: diagnostic criteria].

Schweiz Med Wochenschr. 1996 Mar 16;126(11):421-33.

The sense of smell in primary ciliary dyskinesia.

Thorax. 2018 Oct;73(10):897. doi: 10.1136/thoraxjnl-2018-211620. Epub 2018 Apr 7.

Primary ciliary dyskinesia: can we identify patients with the most severe phenotype?

Minerva Med. 2021 Aug;112(4):518-520. doi: 10.23736/S0026-4806.19.06054-3. Epub 2019 Jun 25.

Improvement in lung health in primary ciliary dyskinesia.

J Paediatr Child Health. 2022 Mar;58(3):526-528. doi: 10.1111/jpc.15550. Epub 2021 May 12.

引用本文的文献

A BEAT-PCD consensus statement: a core outcome set for pulmonary disease interventions in primary ciliary dyskinesia.

ERJ Open Res. 2024 Jan 8;10(1). doi: 10.1183/23120541.00115-2023. eCollection 2024 Jan.

Impact of high- and low-flow nebulised saline on airway hydration and mucociliary transport.

ERJ Open Res. 2023 Jun 12;9(3). doi: 10.1183/23120541.00724-2022. eCollection 2023 May.

Lung function from school age to adulthood in primary ciliary dyskinesia.

Eur Respir J. 2022 Oct 20;60(4). doi: 10.1183/13993003.01918-2021. Print 2022 Oct.

Lower airway clinical outcome measures for use in primary ciliary dyskinesia research: a scoping review.

ERJ Open Res. 2021 Nov 29;7(4). doi: 10.1183/23120541.00320-2021. eCollection 2021 Oct.

Current and Future Treatments in Primary Ciliary Dyskinesia.

Int J Mol Sci. 2021 Sep 11;22(18):9834. doi: 10.3390/ijms22189834.

Primary ciliary dyskinesia: a major player in a bigger game.

Breathe (Sheff). 2020 Jun;16(2):200047. doi: 10.1183/20734735.0047-2020.

[Management of Primary Ciliary Dyskinesia].

Pneumologie. 2020 Nov;74(11):750-765. doi: 10.1055/a-1235-1520. Epub 2020 Sep 25.

Access to medicines for rare diseases: beating the drum for primary ciliary dyskinesia.

ERJ Open Res. 2020 Sep 14;6(3). doi: 10.1183/23120541.00377-2020. eCollection 2020 Jul.

Motile ciliopathies.

Nat Rev Dis Primers. 2020 Sep 17;6(1):77. doi: 10.1038/s41572-020-0209-6.

Proceedings of the 4 BEAT-PCD Conference and 5 PCD Training School.

BMC Proc. 2020 Jun 19;14(Suppl 8):7. doi: 10.1186/s12919-020-00191-3. eCollection 2020.

文献AI研究员

20分钟写一篇综述，助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型，支持多种主流文档格式。

立即体验

相似文献

Hypertonic saline in patients with primary ciliary dyskinesia: on the road to evidence-based treatment for a rare lung disease.

Eur Respir J. 2017 Feb 23;49(2). doi: 10.1183/13993003.02514-2016. Print 2017 Feb.

Rapid Advances in Primary Ciliary Dyskinesia Research. A Brief Update for Pulmonologists.

Am J Respir Crit Care Med. 2019 Jan 15;199(2):136-138. doi: 10.1164/rccm.201807-1390ED.

Outcomes of lung transplantation for primary ciliary dyskinesia and Kartagener syndrome.

J Heart Lung Transplant. 2016 Nov;35(11):1377-1378. doi: 10.1016/j.healun.2016.08.025. Epub 2016 Sep 7.

A randomised controlled trial on the effect of inhaled hypertonic saline on quality of life in primary ciliary dyskinesia.

Eur Respir J. 2017 Feb 23;49(2). doi: 10.1183/13993003.01770-2016. Print 2017 Feb.

Primary ciliary dyskinesia: keep it on your radar.

Thorax. 2018 Feb;73(2):101-102. doi: 10.1136/thoraxjnl-2017-210776. Epub 2017 Nov 13.

Lung function in primary ciliary dyskinesia: breaking the myth that this is a mild disease.

Eur Respir J. 2018 Aug 23;52(2). doi: 10.1183/13993003.01365-2018. Print 2018 Aug.

[Primary ciliary dyskinesia, immotile cilia syndrome, and Kartagener syndrome: diagnostic criteria].

Schweiz Med Wochenschr. 1996 Mar 16;126(11):421-33.

The sense of smell in primary ciliary dyskinesia.

Thorax. 2018 Oct;73(10):897. doi: 10.1136/thoraxjnl-2018-211620. Epub 2018 Apr 7.

Primary ciliary dyskinesia: can we identify patients with the most severe phenotype?

Minerva Med. 2021 Aug;112(4):518-520. doi: 10.23736/S0026-4806.19.06054-3. Epub 2019 Jun 25.

Improvement in lung health in primary ciliary dyskinesia.

J Paediatr Child Health. 2022 Mar;58(3):526-528. doi: 10.1111/jpc.15550. Epub 2021 May 12.

引用本文的文献

A BEAT-PCD consensus statement: a core outcome set for pulmonary disease interventions in primary ciliary dyskinesia.

ERJ Open Res. 2024 Jan 8;10(1). doi: 10.1183/23120541.00115-2023. eCollection 2024 Jan.

Impact of high- and low-flow nebulised saline on airway hydration and mucociliary transport.

ERJ Open Res. 2023 Jun 12;9(3). doi: 10.1183/23120541.00724-2022. eCollection 2023 May.

Lung function from school age to adulthood in primary ciliary dyskinesia.

Eur Respir J. 2022 Oct 20;60(4). doi: 10.1183/13993003.01918-2021. Print 2022 Oct.

Lower airway clinical outcome measures for use in primary ciliary dyskinesia research: a scoping review.

ERJ Open Res. 2021 Nov 29;7(4). doi: 10.1183/23120541.00320-2021. eCollection 2021 Oct.

Current and Future Treatments in Primary Ciliary Dyskinesia.

Int J Mol Sci. 2021 Sep 11;22(18):9834. doi: 10.3390/ijms22189834.

Primary ciliary dyskinesia: a major player in a bigger game.

Breathe (Sheff). 2020 Jun;16(2):200047. doi: 10.1183/20734735.0047-2020.

[Management of Primary Ciliary Dyskinesia].

Pneumologie. 2020 Nov;74(11):750-765. doi: 10.1055/a-1235-1520. Epub 2020 Sep 25.

Access to medicines for rare diseases: beating the drum for primary ciliary dyskinesia.

ERJ Open Res. 2020 Sep 14;6(3). doi: 10.1183/23120541.00377-2020. eCollection 2020 Jul.

Motile ciliopathies.

Nat Rev Dis Primers. 2020 Sep 17;6(1):77. doi: 10.1038/s41572-020-0209-6.

Proceedings of the 4 BEAT-PCD Conference and 5 PCD Training School.

BMC Proc. 2020 Jun 19;14(Suppl 8):7. doi: 10.1186/s12919-020-00191-3. eCollection 2020.