Haider Ali S, Sulhan Suraj, Watson Ian T, Leonard Dean, Arrey Eliel N, Khan Umair, Nguyen Phu, Layton Kennith F
Texas A&M College of Medicine.
UT Houston Medical School, Memorial Hermann.
Cureus. 2017 Feb 16;9(2):e1034. doi: 10.7759/cureus.1034.
Spontaneous intracranial hypotension (SIH) is classified as a decrease in cerebrospinal fluid (CSF) pressure secondary to a CSF leakage and consequent descent of the brain into the foramen magnum. Diagnosing SIH can be difficult due to its overlapping findings with Arnold-Chiari type 1 Malformation (CM1) where the cerebellar tonsils herniate into the foramen magnum. The similarity of both conditions calls for a more reliable imaging technique to localize the CSF leak which could narrow the differential diagnosis and aid in choosing the correct treatment. Here, we present a case of a 28-year-old female, ten weeks post-partum with symptoms similar to SIH. MRI of the brain was remarkable for tonsillar herniation below the foramen magnum. Literature was reviewed for additional neuroradiology techniques that would aid in narrowing our differential diagnosis. Interestingly, computed tomography-, digital subtraction-, and magnetic resonance myelography with intrathecal gadolinium are the preferred techniques for diagnosis of high flow and low flow CSF leaks, respectively. These modalities further aid in choosing the correct treatment while avoiding complications. Literature suggests that treatment for CM1 involves posterior fossa decompression, whereas the mainstay of treatment for SIH involves an epidural blood patch (EBP). Thus, our patient was treated with an EBP and recovered without complication.
自发性颅内低压(SIH)被归类为继发于脑脊液(CSF)漏出及随后脑坠入枕骨大孔导致的脑脊液压力降低。由于其表现与小脑扁桃体疝入枕骨大孔的Arnold-Chiari 1型畸形(CM1)重叠,SIH的诊断可能具有挑战性。这两种情况的相似性需要一种更可靠的成像技术来定位脑脊液漏,这可以缩小鉴别诊断范围并有助于选择正确的治疗方法。在此,我们报告一例28岁产后10周、症状与SIH相似的女性病例。脑部MRI显示小脑扁桃体疝至枕骨大孔以下。我们查阅了文献以寻找有助于缩小鉴别诊断范围的其他神经放射学技术。有趣的是,计算机断层扫描、数字减影以及鞘内注射钆剂的磁共振脊髓造影分别是诊断高流量和低流量脑脊液漏的首选技术。这些检查方法有助于选择正确的治疗方法,同时避免并发症。文献表明,CM1的治疗包括后颅窝减压,而SIH的主要治疗方法是硬膜外血贴(EBP)。因此,我们的患者接受了EBP治疗,康复且无并发症。