Saeki Isamu, Ueno Yu, Mukai Wataru, Imaji Reisuke, Akiyama Takashi
Department of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, Japan.
Department of Pediatric Surgery, Hiroshima City Hospital, 7-33 Motomachi Naka-ku, Hiroshima-shi, Hiroshima 730-8518, Japan; Chugoku-Shikoku Pediatric Surgical Partners Organization, Japan.
Case Rep Pediatr. 2017;2017:2074387. doi: 10.1155/2017/2074387. Epub 2017 Mar 12.
. Situs inversus is a rare congenital anomaly with a reported incidence of only 1 in 5,000 to 10,000 live births. Congenital duodenal stenosis complicated with situs inversus is an even rarer entity. . A 1-year-old girl with situs inversus who had undergone a hemi-Fontan procedure against a single ventricle in our hospital was referred to our department for vomiting and failure to thrive. An upper gastrointestinal contrast study and endoscopy revealed duodenal stenosis. A transumbilical radical operation as a minimally invasive surgery was successfully performed. After the surgery, she stopped vomiting, and the postoperative course was uneventful with good cosmetic results. . To our knowledge, this is the first report of transumbilical surgery for congenital duodenal stenosis with situs inversus as minimally invasive surgery. Transumbilical surgery to situs inversus patient can be performed safely and lead to good cosmetic outcome.
内脏反位是一种罕见的先天性异常，据报道其在活产婴儿中的发生率仅为1/5000至1/10000。先天性十二指肠狭窄合并内脏反位则更为罕见。一名1岁内脏反位女童曾在我院接受针对单心室的半Fontan手术，因呕吐和发育不良被转诊至我科。上消化道造影检查和内镜检查显示十二指肠狭窄。成功实施了经脐根治性手术，作为微创手术。术后，她停止呕吐，术后过程顺利，美容效果良好。据我们所知，这是首例将经脐手术作为微创手术治疗先天性十二指肠狭窄合并内脏反位的报道。经脐手术对内脏反位患者可安全实施，并能取得良好的美容效果。
