先天性完全性心脏传导阻滞合并左心发育不全综合征
Hypoplastic Left Heart Syndrome with Congenital Complete Heart Block.
作者信息
Al-Kubaisi Maytham, Aly Safwat A, Mohammad Nijres Bassel, Awad Sawsan
机构信息
Rush University Medical Center, Rush Center for Congenital Heart Disease, 1653 W. Congress Pkwy, Pavilion Building, Suite 654, Chicago, IL, USA.
出版信息
Pediatr Cardiol. 2017 Aug;38(6):1305-1308. doi: 10.1007/s00246-017-1631-8. Epub 2017 May 17.
Congenital complete atrioventricular block (CCAVB) is a rare condition with an incidence of 1 of 20,000 live births. Hypoplastic left heart syndrome (HLHS) occurs more frequently than CCAVB and occurs in 1 of 5000 live births. HLHS in association with CCAVB is exceedingly rare. In this report, we describe a rare case of HLHS and CCAVB diagnosed in utero. Postnatal diagnosis, management and outcome are presented as well as review of the medical literature.
先天性完全性房室传导阻滞（CCAVB）是一种罕见疾病，活产儿中的发病率为两万分之一。左心发育不全综合征（HLHS）的发病率高于CCAVB，为五千分之一。HLHS合并CCAVB极为罕见。在本报告中，我们描述了一例在子宫内诊断出的HLHS合并CCAVB的罕见病例。同时介绍了产后诊断、治疗及结果，并对医学文献进行了综述。
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