van Heerden J A, Sizemore G W, Carney J A, Brennan M D, Sheps S G
Surgery. 1985 Aug;98(2):363-6.
Our treatment philosophy for the management of the adrenal glands in patients with multiple endocrine neoplasia, type IIa has been bilateral total adrenalectomy. In the patient described, exceptional and pressing reasons necessitated preservation of adrenocortical function. Bilateral pheochromocytomas were resected with preservation of the adrenal cortices. Adrenocortical function was normal 36 months after resection. Although the patient remained symptom free, elevated basal immunoreactive plasma calcitonin levels suggested the presence of residual or metastatic medullary thyroid carcinoma. There was no evidence of recurrent pheochromocytoma.
我们对于IIa型多发性内分泌腺瘤病患者肾上腺管理的治疗理念一直是双侧肾上腺全切术。在所描述的该患者中,特殊且紧迫的原因使得有必要保留肾上腺皮质功能。双侧嗜铬细胞瘤在保留肾上腺皮质的情况下被切除。切除术后36个月肾上腺皮质功能正常。尽管患者仍无症状,但基础免疫反应性血浆降钙素水平升高提示存在残余或转移性甲状腺髓样癌。没有复发性嗜铬细胞瘤的证据。