[Hypertrophic cardiomyopathies--present knowledge].

Hypertrophic cardiomyopathies are observed under 3 anatomic forms: septal, concentric, apical. Their pathogenesis is still unknown. Theorie involving catecholamine appears the most acceptable. Among the diagnostic signs, septum cellular disorganization is the precise anatomic criteria. Obstructive cardiomyopathy is no longer an isolated entity, but a form of transition between the three anatomic forms. Pronostic is dominated by sudden death; amiodarone is the best preventive treatment.