Madala Jayakiran, Bashamalla Rithika, Kumar M Praveen
Department of Oral Pathology and Microbiology, Mamata Dental College, Khammam, Telangana, India.
J Oral Maxillofac Pathol. 2017 May-Aug;21(2):260-263. doi: 10.4103/jomfp.JOMFP_143_17.
Pemphigus vulgaris is an autoimmune bullous disease involving both the skin and mucosal areas, which is characterized by intraepithelial flaccid blisters and erosions. The pathogenesis of this disease is not yet completely established, but novel intuitions into its pathogenesis have recently been published. An unanswered question in its pathophysiology is the mechanism of acantholysis or loss of keratinocyte cell adhesion. Acantholysis seems to result from a communal action of autoantibodies against numerous keratinocyte self-antigens, of which desmogleins 1 and 3, desmocollins and nondesmosome components, such as the mitochondrion, might take part in the disease initiation. Lately, apoptosis was described as a possible underlying mechanism of acantholysis. Likewise, apoptolysis is assumed to be the association between suprabasal acantholytic and cell death pathways. Hence, the present review focuses on the current concepts in the pathogenesis of the pemphigus in a nutshell.
寻常型天疱疮是一种累及皮肤和黏膜区域的自身免疫性大疱性疾病,其特征为上皮内松弛性水疱和糜烂。该疾病的发病机制尚未完全明确,但最近已发表了有关其发病机制的新见解。其病理生理学中一个尚未解决的问题是棘层松解或角质形成细胞细胞黏附丧失的机制。棘层松解似乎是针对多种角质形成细胞自身抗原的自身抗体共同作用的结果,其中桥粒芯糖蛋白1和3、桥粒胶蛋白以及非桥粒成分(如线粒体)可能参与疾病的起始。最近,细胞凋亡被描述为棘层松解的一种可能潜在机制。同样,凋亡被认为是棘层松解上方区域与细胞死亡途径之间的关联。因此,本综述简要聚焦于天疱疮发病机制的当前概念。