Flipsen Mark, Ham John S, van der Zwan Arnard L, Mader Konrad
Department of Orthopaedics, OLVG, Amsterdam, The Netherlands.
Department of Orthopaedic, Trauma, and Spine Surgery, Section Upper Extremity, Asklepios Klinik Altona, Hamburg, Germany.
J Pediatr Orthop B. 2018 Jul;27(4):289-295. doi: 10.1097/BPB.0000000000000496.
Multiple hereditary exostoses (MHE) are a rare disorder characterized by the growth of bony protrusions. Elbow involvement is found in a considerable number of patients and varies from the presence of a simple osteochondroma to severe forearm deformities and radial head dislocation. Patients encounter a variety of symptoms, for example, pain, functional impairment, and cosmetic concerns. Several types of surgical procedures, therefore, can be offered, ranging from excision of symptomatic osteochondromas to challenging reconstructions. In this paper, we will discuss the essential basics of visualizing, planning, and treatment options of forearm deformities in MHE. In more detail, we will describe our current surgical technique as a salvage procedure for Masada type II forearm deformities in patients with MHE.
多发性遗传性骨软骨瘤(MHE)是一种罕见的疾病,其特征是骨突起生长。相当多的患者会出现肘部受累,表现从单纯骨软骨瘤到严重的前臂畸形和桡骨头脱位不等。患者会出现多种症状,例如疼痛、功能障碍和外观问题。因此,可以提供几种类型的手术方法,从切除有症状的骨软骨瘤到具有挑战性的重建手术。在本文中,我们将讨论MHE中前臂畸形的可视化、规划和治疗选择的基本要点。更详细地说,我们将描述我们目前作为MHE患者Masada II型前臂畸形挽救手术的手术技术。