休斯-斯托文综合征揭示了白塞病的存在。
Hughes-Stovin syndrome revealing the presence of Behçet's Disease.
作者信息
Kechida Melek, Yaacoubi Sondes, Zrig Ahmed, Jomaa Walid, Klii Rim, Hammami Sonia, Khochtali Ines
机构信息
Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia.
Department of Radiology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia.
出版信息
Caspian J Intern Med. 2017 Fall;8(4):332-334. doi: 10.22088/cjim.8.4.332.
BACKGROUND
Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen.
CASE PRESENTATION
We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet's disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome.
CONCLUSION
Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet's disease.
背景
休斯-斯托文综合征（HSS）是一种罕见的临床疾病，其特征为深静脉血栓形成以及多个肺和/或支气管动脉瘤。也可见体循环中的动脉瘤。
病例报告
我们报告了首例患有主动脉瘤的HSS病例，患者为一名55岁男性，最初表现为深静脉血栓形成。鉴于有复发性口腔溃疡和生殖器溃疡病史，诊断为显示白塞病的HSS。治疗包括每日3次静脉注射甲泼尼龙（1g），随后口服泼尼松（每日1mg/kg）以及每6个月静脉注射1次环磷酰胺。口服抗凝治疗暂停3个月，之后停药，效果良好。
结论
休斯-斯托文综合征中的体循环动脉瘤是一种值得了解的并发症，可能提示白塞病。
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