Zhang Fengtian, Yu Xiaolong, Zeng Jin, Dai Min
Department of Orthopedics, The First Affiliated Hospital of Nanchang University, Artificial Joints Engineering and Technology Research Center of Jiangxi Province, Nanchang, Jiangxi, China.
Medicine (Baltimore). 2017 Nov;96(47):e8759. doi: 10.1097/MD.0000000000008759.
Teratomas, which most frequently affect adult females, are the most common type of germ cell tumor, it always comprises derivatives of at least 2 germ layers. The most common site of primary teratomas is the ovary. Sacrococcygeal teratomas (SCTs), which are exceedingly rare in adults, are generally found in newborns or children.
A 39-year-old woman presented to our clinic with a 1-year history of gradually aggravated difficulty in micturition and defecation, and a tumor in her right buttock present since birth. Appropriate preoperative examinations showed a large (15.6 cm × 12.2 cm × 30.0 cm) multicystic SCT.
Histologic examination confirmed a mucinous tumor arising in a giant SCT.
Abdominoperineal rectal resection was performed.
The patient recovered well and was discharged on day 33 of admission.
We report the first case of a mucinous tumor arising in an SCT, in which the teratoma presented mature tissue elements derived only from the endodermal germ layer (keratinous debris).
畸胎瘤是最常见的生殖细胞肿瘤类型,最常发生于成年女性,总是包含至少两个胚层的衍生物。原发性畸胎瘤最常见的部位是卵巢。骶尾部畸胎瘤(SCT)在成年人中极为罕见,通常见于新生儿或儿童。
一名39岁女性因排尿和排便困难逐渐加重1年,且自出生以来右臀部有一肿瘤,前来我院就诊。适当的术前检查显示为一个巨大的(15.6厘米×12.2厘米×30.0厘米)多囊性骶尾部畸胎瘤。
组织学检查证实为巨大骶尾部畸胎瘤内发生的黏液性肿瘤。
行腹会阴直肠切除术。
患者恢复良好,入院第33天出院。
我们报告了首例骶尾部畸胎瘤内发生的黏液性肿瘤病例,该畸胎瘤呈现仅来自内胚层生殖层(角质碎屑)的成熟组织成分。