Schachinger Florian, Girsch Werner, Farr Sebastian
* Department of Pediatric Orthopedics and Adult Foot and Ankle Surgery, Orthopedic Hospital Speising, Vienna, Austria.
J Hand Surg Asian Pac Vol. 2018 Mar;23(1):153-157. doi: 10.1142/S2424835518720116.
Ulnar longitudinal deficiency (ULD) is a rare congenital disease of the upper limb. The deformities caused by ULD can be very challenging and may compromise hand function during daily activities. Although the first surgical intervention dates back to the year 1952 there is still no gold standard for treating this uncommon disorder. Two children aged 16 and 3 years with ULD Bayne Type II (partial ulna aplasia) were diagnosed and treated at our department with single bone forearm surgery to achieve stability and improve function using a modified surgical method. For the purpose of an additional gain in limb length and improved cosmesis we used an Ilizarov external fixator for soft tissue distraction including radius distalization prior to the creation of the single bone forearm. This new technique and results are presented and discussed.
尺骨纵向发育不全（ULD）是一种罕见的上肢先天性疾病。ULD所导致的畸形极具挑战性，可能会影响日常活动中的手部功能。尽管首次手术干预可追溯到1952年，但对于这种罕见疾病的治疗仍没有金标准。我们科室诊断并治疗了两名分别为16岁和3岁的患有ULD贝氏II型（部分尺骨发育不全）的儿童，采用改良手术方法进行单骨前臂手术以实现稳定性并改善功能。为了额外增加肢体长度并改善美观，我们在构建单骨前臂之前使用Ilizarov外固定器进行软组织牵张，包括桡骨远端移位。本文展示并讨论了这项新技术及结果。
