Department of Pediatrics, Section of Hematology/Oncology, Baylor College of Medicine, Houston, TX.
Texas Children's Cancer and Hematology Centers, Houston, TX.
Blood Adv. 2018 Feb 27;2(4):454-461. doi: 10.1182/bloodadvances.2017010660.
Eltrombopag is currently the only US Food and Drug Administration-approved thrombopoietin receptor agonist for the treatment of chronic immune thrombocytopenia (ITP) in children. This oral, once-per-day therapy has shown favorable efficacy and adverse effect profiles in children. Two multicenter, double-blind, placebo controlled clinical trials (PETIT [Efficacy and Safety Study of Eltrombopag in Pediatric Patients With Thrombocytopenia From Chronic Idiopathic Thrombocytopenic Purpura (ITP)] and PETIT2 [Study of a New Medication for Childhood Chronic Immune Thrombocytopenia (ITP), a Blood Disorder of Low Platelet Counts That Can Lead to Bruising Easily, Bleeding Gums, and/or Bleeding Inside the Body]) demonstrated efficacy in raising platelet counts, reducing bleeding, and reducing the need for concomitant ITP therapies with relatively few adverse effects. The most commonly reported drug-related adverse effects include headache, nausea, and hepatobiliary laboratory abnormalities. Long-term safety data in children are limited, and studies in adults have not revealed a clinically significant increased incidence of thrombosis, marrow fibrosis, or cataract formation. Eltrombopag has also been approved for treating refractory severe aplastic anemia (AA) and has potential for expanded use in ITP and severe AA as well as in other conditions associated with thrombocytopenia.
依洛尤单抗是目前唯一获得美国食品药品监督管理局批准用于治疗儿童慢性免疫性血小板减少症(ITP)的血小板生成素受体激动剂。这种口服、每日一次的治疗方法在儿童中显示出良好的疗效和不良作用谱。两项多中心、双盲、安慰剂对照的临床试验(PETIT[依洛尤单抗治疗儿童慢性特发性血小板减少性紫癜(ITP)血小板减少症的疗效和安全性研究]和 PETIT2[研究一种用于治疗儿童慢性免疫性血小板减少症(ITP)的新药,一种血小板计数低的血液疾病,可导致容易瘀伤、牙龈出血和/或体内出血])证明了其升高血小板计数、减少出血和减少同时进行 ITP 治疗的效果,且不良作用相对较少。最常报告的与药物相关的不良影响包括头痛、恶心和肝胆实验室异常。儿童的长期安全性数据有限,且成人研究并未显示血栓形成、骨髓纤维化或白内障形成的发生率有临床意义增加。依洛尤单抗也已被批准用于治疗难治性严重再生障碍性贫血(AA),并有可能在 ITP 和严重 AA 以及其他与血小板减少症相关的疾病中扩大应用。