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复发性特发性神经视网膜炎作为非典型视神经炎的一种表现形式:病例报告及文献综述

Recurrent idiopathic neuroretinitis as a spectrum of atypical optic neuritis: a case report and literature review.

作者信息

Viturino Marina Gonçalves Monteiro, Moura Frederico Castelo

机构信息

Department of Ophthalmology, Universidade de Campinas, Campinas, SP, Brazil.

Department of Ophthalmology, Universidade de São Paulo, São Paulo, SP, Brazil.

出版信息

Arq Bras Oftalmol. 2018 Jan-Feb;81(1):70-72. doi: 10.5935/0004-2749.20180016.

Abstract

Recurrent idiopathic neuroretinitis is an inflammatory optic neuropathy characterized by optic nerve edema and macular star, associated with painless and recurrent episodes of visual loss, poor visual prognosis, and visual field defects related to nerve fiber layer injury. The disorder is sometimes mistaken for atypical optic neuritis. However, early diagnosis is important for visual recovery. Long-term immunosuppression has been shown to reduce the rate of recurrence and protect against severe and irreversible vision loss.

摘要

复发性特发性神经视网膜炎是一种炎症性视神经病变,其特征为视神经水肿和黄斑星芒状渗出,伴有无痛性且反复发作的视力丧失、视力预后不良以及与神经纤维层损伤相关的视野缺损。该疾病有时会被误诊为非典型视神经炎。然而,早期诊断对于视力恢复很重要。长期免疫抑制已被证明可降低复发率,并预防严重且不可逆的视力丧失。

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引用本文的文献

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Review of atypical optic neuritis.非典型视神经炎综述
Neurol Sci. 2025 Apr;46(4):1555-1564. doi: 10.1007/s10072-024-07895-w. Epub 2024 Dec 18.
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Bilateral Idiopathic Neuroretinitis.双侧特发性神经视网膜炎。
Diagnostics (Basel). 2024 Oct 26;14(21):2386. doi: 10.3390/diagnostics14212386.

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