Pérez Tatiana Marcela, García Sandra Milena, Velasco Martha Lucía, Sánchez Angela Paola
Programa de Residencia de Radiología, Universidad de la Sabana, Campus del Puente del Común, Km. 7, Autopista Norte de Bogotá, Chía, Cundinamarca, Colombia.
Departamento de Radiología. Fundación Clínica Shaio, Diagonal 115a # 70C-75, Bogotá, Colombia.
Radiol Case Rep. 2017 Nov 17;13(1):35-38. doi: 10.1016/j.radcr.2017.10.001. eCollection 2018 Feb.
Interrupted aortic arch is an extremely rare congenital malformation representing about 1% of congenital heart disease. Early symptoms usually occur early in the neonatal period and clinical deterioration is often rapid and long-term prognosis is limited. Nonetheless, this condition has been identified later in adult life in rare cases. We report a case in an adult male with absence of hypertension history and no further cardiac compromise, with a severe posterior chest pain alongside dyspnea and sweating. Computed tomography angiography revealed interrupted aortic arch type A, bivalve aorta, hemopericardium, aortic dissection Stanford A, and important collateral circulation.
主动脉弓中断是一种极其罕见的先天性畸形,约占先天性心脏病的1%。早期症状通常在新生儿期早期出现,临床病情恶化往往迅速,长期预后有限。尽管如此,这种情况在成年期的罕见病例中也有发现。我们报告一例成年男性病例,该患者无高血压病史,无进一步的心脏损害,伴有严重的胸痛、呼吸困难和出汗。计算机断层扫描血管造影显示为A型主动脉弓中断、双瓣主动脉、心包积血、斯坦福A型主动脉夹层以及重要的侧支循环。