LaPar Damien J, Baird Christopher W
1 Columbia University Vagelos College of Physicians and Surgeons, New York, NY, USA.
2 Harvard Medical School, Boston Children's Hospital, Boston, MA, USA.
Semin Cardiothorac Vasc Anesth. 2018 Sep;22(3):278-284. doi: 10.1177/1089253218776664. Epub 2018 May 18.
Interrupted aortic arch (IAA) is a rare congenital anomaly with several anatomical variants and is often associated with other intracardiac and/or extracardiac congenital anomalies. Historically, associated with high early mortality, outcomes for this anomaly have improved in recent eras with advances in perioperative and anesthesia management and refinements in surgical technique. This review provides a description of surgical anatomy, anatomical classifications, and associated congenital lesions as well as an examination of the perioperative and surgical management of IAA in the contemporary surgical era.
主动脉弓中断(IAA)是一种罕见的先天性异常,有多种解剖变异,常与其他心内和/或心外先天性异常相关。历史上,这种异常与早期高死亡率相关,随着围手术期和麻醉管理的进步以及手术技术的改进,近年来其治疗结果有所改善。本综述描述了手术解剖、解剖分类和相关先天性病变,并探讨了当代手术时代主动脉弓中断的围手术期和手术管理。