Krishnan Shyam Sundar, Nigam Pulak, Mohanty Poonam, Vasudevan Madabhushi Chakravarthy, Kameswaran Mohan
Dr. Achantha Lakshmipathi Neurosurgical Centre, Post Graduate Institute of Neurological Surgery, Voluntary Health Services Multi-Speciality Hospital & Research Centre, TTTI Post, Taramani, Adyar, Chennai, Tamil Nadu, 600113, India.
Madras ENT Research Foundation, No. 1, 2nd Cross Street, RA Puram, Chennai, Tamil Nadu, 600028, India.
Childs Nerv Syst. 2018 Sep;34(9):1745-1752. doi: 10.1007/s00381-018-3829-3. Epub 2018 Jun 8.
Auditory brainstem implant (ABI), a standard technique in treatment of profound sensorineural hearing loss in patients with neurofibromatosis 2, is now being increasingly employed in children with congenital bilateral sensorineural hearing loss, as in Michele's deformity. A detailed knowledge of the relevant surgical anatomy of the lateral recess and its anatomical landmarks including the flocculus, the choroid plexus and the root entry zones of facial-vestibulocochlear and glossopharyngeal-vagus nerve complexes and their anatomical variants is mandatory, as it is the conduit for electrode array placement. The placement of electrode may be eased or impeded by these variations.
Thirty-two children with congenital bilateral hearing loss underwent surgery through retromastoid suboccipital approach for placement of auditory brainstem implant. The preoperative anatomy was reviewed in detail during procedure and again later in the operative videos.
The flocculus was classified into four grades based on its anatomy and relations. Among these, grade II (11 children) was the commonest while grade IV (five children) was least common. Choroid plexus was variable in size across grades of flocculus. Difficulty in defining the anatomy was significantly more (p value = 0.003) in the group with higher grade flocculus (grade III and IV) than in lower grade flocculus (grade I and II).
The flocculus in these patients is classifiable into one of the four grades and the surgical nuances such as difficulty in defining the anatomy for placement of ABI are dependent on the characteristics exhibited by the floccular anatomy and relations.
听觉脑干植入术(ABI)是治疗神经纤维瘤病2型患者严重感音神经性听力损失的标准技术,现在越来越多地应用于患有先天性双侧感音神经性听力损失的儿童,如米歇尔畸形。详细了解外侧隐窝的相关手术解剖结构及其解剖标志,包括绒球、脉络丛以及面听神经和舌咽迷走神经复合体的神经根进入区及其解剖变异是必不可少的,因为它是电极阵列放置的通道。这些变异可能会使电极放置变得容易或受阻。
32例先天性双侧听力损失患儿通过乳突后枕下入路进行听觉脑干植入术。在手术过程中详细回顾了术前解剖结构,并在手术视频后期再次进行回顾。
根据绒球的解剖结构和关系将其分为四个等级。其中,II级(11例患儿)最为常见,IV级(5例患儿)最不常见。脉络丛的大小在不同等级的绒球中各不相同。与较低等级绒球(I级和II级)相比,较高等级绒球(III级和IV级)组在界定解剖结构时的困难明显更大(p值 = 0.003)。
这些患者的绒球可分为四个等级之一,并且诸如在放置ABI时界定解剖结构困难等手术细微差别取决于绒球解剖结构和关系所表现出的特征。