Erinanc Hilal, Ozulku Mehmet, Terzi Aysen
Konya Uygulama ve Arastırma Hastanesi, Pathology Department, Medicine Faculty, Baskent University, Selcuklu, Konya, Turkey.
Konya Uygulama ve Arastırma Hastanesi, Cardiothoracic Surgery Department, Medicine Faculty, Baskent University, Selcuklu, Konya, Turkey.
Case Rep Oncol Med. 2018 Jun 5;2018:3094616. doi: 10.1155/2018/3094616. eCollection 2018.
Primary leiomyosarcomas of vascular origin are rare tumors. They frequently arise within the inferior vena cava; however, the peripheral vein was also affected. To date, only a few hundred cases have been reported in the world literature. Although it is an extremely aggressive tumor, the symptoms may be unspecific, especially in the lower extremities. In this report, we present a case of primary vascular leiomyosarcoma, arising from the short saphenous vein, with symptoms mimicking thrombus in the initial diagnosis. The diagnosis of leiomyosarcomas was confirmed by standard H&E staining and immunohistochemical staining. Recurrence of the tumor has been observed five years after surgical treatment. Due to its rarity, experience in the management of this type of tumor is limited. The mainstay of treatment for these tumors is complete surgical resection. The purpose of the presented case is to discuss the clinicopathological features and management options of this tumor, under the light of the most recent literatures.
原发性血管源性平滑肌肉瘤是罕见肿瘤。它们常发生于下腔静脉内；然而，外周静脉也可受累。迄今为止，世界文献中仅报道了几百例。尽管它是一种极具侵袭性的肿瘤，但其症状可能不具特异性，尤其是在下肢。在本报告中，我们呈现了一例起源于小隐静脉的原发性血管平滑肌肉瘤病例，其初始诊断时症状类似血栓。平滑肌肉瘤的诊断通过标准苏木精-伊红染色和免疫组织化学染色得以证实。手术治疗五年后观察到肿瘤复发。由于其罕见性，这类肿瘤的治疗经验有限。这些肿瘤的主要治疗方法是完整手术切除。本病例的目的是根据最新文献探讨该肿瘤的临床病理特征及治疗选择。
