Liu Qinqin, Fang Lu, Li Bo
Department of liver Surgery.
Department of Burn and Plastic Surgery, West China Hospital, Sichuan University, Chengdu, China.
Medicine (Baltimore). 2018 Nov;97(44):e13109. doi: 10.1097/MD.0000000000013109.
Desmoid fibromatosis is a rare benign neoplasm arising from musculoaponeurotic structures with the potential to infiltrate local tissues and recur locally. While the commonly affected regions are the shoulder, chest wall and back, thigh, head and neck, localization in the foot is rare and only a few cases have been reported. Deep-seated lesions of foot tend to spread along the fascia and nerve or tendon sheaths.
We present a case of a 41-year-old female with a 3 years history of a slowly enlarging painful mass in the right foot.
Desmoid fibromatosis was diagnosed based on clinical manifestations, imaging findings and pathological examinations.
The patient was treated by local incomplete resection.
The patient recovered well postoperatively and was well followed up at our outpatient department with no evidence of recurrence during 16 months of follow-up after local excision.
Surgical excision is recommended for symptomatic lesions located in the foot. However, it is difficult to excise thoroughly and periodic follow-up is needed to monitor for recurrence. Further study is warranted to determine whether patients benefit more from function preservation instead of complete resection.
韧带样纤维瘤病是一种罕见的良性肿瘤,起源于肌筋膜结构,有浸润局部组织并局部复发的可能。虽然常见受累部位是肩部、胸壁和背部、大腿、头颈部,但足部定位罕见,仅有少数病例报道。足部深部病变往往沿筋膜及神经或腱鞘蔓延。
我们报告一例41岁女性,右足有一缓慢增大的疼痛性肿块,病史3年。
根据临床表现、影像学检查及病理检查诊断为韧带样纤维瘤病。
患者接受局部不完全切除术治疗。
患者术后恢复良好,在我院门诊进行了良好的随访,局部切除术后16个月的随访期间无复发迹象。
对于足部有症状的病变,建议手术切除。然而,彻底切除困难,需要定期随访以监测复发情况。有必要进一步研究以确定患者从功能保留而非完全切除中获益是否更多。