Park Hyojung, Song Jinyoung, Huh June, Kang I-Seok, Jun Tae-Gook, Yang Ji-Hyuk
Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine.
Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine.
Korean J Thorac Cardiovasc Surg. 2018 Dec;51(6):403-405. doi: 10.5090/kjtcs.2018.51.6.403. Epub 2018 Dec 5.
This case report concerns a young patient with an extremely rare combination of d-transposition of the great arteries (d-TGA) and anomalous origin of the right subclavian artery. In our patient, the right subclavian artery originated from the pulmonary artery, which is why he did not show reversed differential cyanosis. We conclude that the presence of an aortic arch anomaly should be considered in patients with d-TGA who do not present with reversed differential cyanosis. A further imaging work-up, including computed tomography or magnetic resonance imaging, might be helpful.
本病例报告涉及一名年轻患者,其患有极为罕见的大动脉d型转位(d-TGA)与右锁骨下动脉异常起源的组合。在我们的患者中,右锁骨下动脉起源于肺动脉,这就是他未出现反向差异性发绀的原因。我们得出结论,对于未出现反向差异性发绀的d-TGA患者,应考虑存在主动脉弓异常的情况。进一步的影像学检查,包括计算机断层扫描或磁共振成像,可能会有所帮助。