Cuneo Antonio, Foà Robin
Hematology, Department of Medical Sciences, University of Ferrara, Italy.
Hematology, Department of Cellular Biotechnologies and Hematology, Policlinico Umberto 1, 'Sapienza' University, Rome, Italy.
Mediterr J Hematol Infect Dis. 2019 Mar 1;11(1):e2019024. doi: 10.4084/MJHID.2019.024. eCollection 2019.
Treatment of relapsed/refractory (R/R) chronic lymphocytic leukemia (CLL) has dramatically improved thanks to the development of mechanism-driven agents including drugs that inhibit kinases in the BCR pathway or BCL2. The treating physician has now the opportunity to decide i) which patient can be still offered chemoimmunotherapy as salvage treatment, ii) which patient at relapse is a candidate to receiving, continuous treatment with ibrutinib, idelalisib and rituximab or venetoclax and iii) which patient may benefit from a fixed-duration treatment using the BCL2 antagonist venetoclax in association with rituximab. Ibrutinib is the most actively investigated drug in R/R CLL and data at a 7-year follow-up were reported, showing durable efficacy and favorable efficacy profile. The patients with cardiac disease, hypertension, and anticoagulant therapy are not ideal candidates for continuous therapy with this agent. Idelalisib and rituximab were tested in patients with unfavorable characteristics including cytopenias. The short follow-up and treatment-emergent adverse events limit its role to patients unlikely to get a benefit with other agents. Venetoclax and rituximab is the only effective chemo-free approach for the treatment of R/R with a fixed duration (up to 24 months) schedule capable of inducing deep responses in the majority of cases with a reassuring safety profile. While a deep knowledge of the growing body of scientific evidence is required to inform and guide the appropriate treatment choice and management, physicians cannot disregard the growing problem of sustainability.
由于包括抑制BCR通路激酶或BCL2的药物在内的机制驱动药物的发展,复发/难治性(R/R)慢性淋巴细胞白血病(CLL)的治疗有了显著改善。现在,主治医生有机会决定:i)哪些患者仍可接受化疗免疫疗法作为挽救治疗;ii)哪些复发患者适合接受依鲁替尼、艾代拉利司和利妥昔单抗或维奈托克的持续治疗;iii)哪些患者可能受益于使用BCL2拮抗剂维奈托克联合利妥昔单抗的固定疗程治疗。依鲁替尼是R/R CLL中研究最活跃的药物,已有7年随访数据报道,显示出持久疗效和良好的疗效特征。患有心脏病、高血压和正在接受抗凝治疗的患者并非该药物持续治疗的理想人选。艾代拉利司和利妥昔单抗已在包括血细胞减少等不良特征的患者中进行了测试。随访时间短和治疗中出现的不良事件限制了其在不太可能从其他药物中获益的患者中的应用。维奈托克和利妥昔单抗是唯一一种有效的无化疗方法,用于治疗R/R,采用固定疗程(长达24个月)方案,能够在大多数情况下诱导深度缓解,且安全性令人放心。虽然需要深入了解不断增加的科学证据以指导适当的治疗选择和管理,但医生不能忽视日益严重的可持续性问题。